Syndrome Goodpasture esithi: Ibangela, Iimpawu kunye Iindlela Treatment

Goodpasture kaThixo syndrome - isifo esinqabileyo samathambo into ihamba kunye kwisizukulwana omzimba Nedlac ezihlasela kwiiseli ze imiphunga kunye nezintso. isifo efanayo ubukhulu becala kuchaphazela abantu abaphakathi kweminyaka eli-12 neli-35 ubudala. Kukholelwa ukuba izigulane ezithile abe olungaka ngezemvelo isiphazamiso onjalo.

syndrome Goodpasture esithi: ezibangela izifo

Kakade ke, umguli kwabantu yofuzo ukuya sifo. Noko ke, kukho izinto engabangela ukusabela sokuhlasela.

Kunye nophuhliso sifo amajoni omzimba ukhupha izilwa ukuba ahlasele inwebu carcinomas le emithanjeni of alveoli pulmonary kunye tubules sezintso. Ngenxa yale nkqubo abachaphazelekayo waziqhawula emithanjeni, ibangela ukopha lwangaphakathi kunye neempawu ezinxulumene.

Kuba okokuqala sifo iye yabhalwa ngowe-1919. Kodwa kule mini akwaziwa into ichukumisa impendulo omzimba. Kukholelwa ukuba Goodpasture engqondweni inxulunyaniswa kunye nezifo ezosulelayo. Ngamanye amaxesha okanye ipoti ye-sisifo esibangelwa iikhemikhali ezithile, ibinza. It ababhala iimeko ezininzi apho syndrome waqalisa ukuba emva kokuthatha amayeza.

syndrome Goodpasture esithi: iimpawu

Ngokuqhelekileyo, iimpawu yokuqala isixokelelwano sokuphefumla. Isigulane ikhalazela iintlungu esifubeni, rhoqo ukhohlokhohlo kwakunye nokubamba-bamba umphefumlo kwi ngamandla. Ngokutsho hemoptysis iqala kunye nophuhliso sifo. Imiphunga zwa ukutswina ezimanzi okanye ezomileyo. Isigulane bangase ukudinwa rhoqo ukozela. Maxa wambi kukho ubunzima ilahleko kakhulu ngenxa ukuhla mass kwezihlunu. Ngokwahlukileyo inkolelo ethandwayo, ezi ngcanjana emehlweni azichaphazeleki sifo.

Ekubeni kukho legazi ezincinane ezinkulu, uphawu elilandelayo - yinto anemia, okanye nezinye. Xa uhlolisisa isigulana, oko kunokubonwa ukuba ulusu lwakhe lisuke labuna kakhulu. Kukho cyanosis ye inwebu yangaphakathi. Kwezinye iimeko, iindumbisa ubuso kuvela. Iqondo lobushushu ngokubanzi kakhulu.

Iimpawu zesi sifo izintso kuvela kancinci kamva. ngamana phawula Ukukhethwa encinci igazi yokuchama. ukusilela kwezintso sanda ngokukhawuleza kwaye lukhatshwa iimpawu zalo.

syndrome Goodpasture esithi: iindlela zokuxilonga

Ukuze wenze sifo, ugqirha kufuneka balujongisise ngenyameko isigulane ukubona iziphumo neemvavanyo ECG. Ngokubanzi, uhlalutyo igazi ingabonwa deficiency anemia zentsimbi kunye nokwanda leukocyte count, landa ESR. Urinalysis ibona umchamo ngezixa amakhulu protein kunye neeseli ezibomvu zegazi. Kufuneka ngokuqinisekileyo uphando isikhohlela, njengokuba kubhaliwe kwakhona kufunyenwe iiseli ezibomvu. Kuya kuba luncedo kunye spirography kunceda ukubona zolwaphulo of nokuphefumla lwangaphandle. Yabelwe kwakhona ECG isifundo iigesi igazi,-x-reyi kunye biopsy le nyama ezonakeleyo, nto leyo eyenza kube lula ukubeka isifo esichazayo.

syndrome Goodpasture esithi: Kuxakekwe ngonyango

Enyanisweni, i-ALS izigulane ezinjalo elingamncediyo. Kwaye eyona nto ibalulekileyo apha - ixesha ukufumanisa isifo kwaye uqale unyango ngokukhawuleza.

Ngelishwa, iziyobisi ezithile izifo ezifana ungekho. Kodwa ke waphawula ukuba kwiimeko ezininzi, umsebenzi olwaneleyo unyango syndrome kudambe kwisithuba seenyanga 6-9. Ukuba uyakwazi ukunqanda uphuhliso isifo sezintso miphungeni, isigulane unako kusinda. Ngokuqhelekileyo, oogqirha amisele inani yokufumana corticosteroids. Plasmapheresis lwenziwa, ukuba kuyimfuneko - ukutofelwa igazi , yaye kidney abohlukeneyo. Ukuze ukumisa uphuhliso kwegazi kunye deficiency yentsimbi fill ukumisela amayeza afanelekileyo. Kodwa ngamanye amaxesha, kwiimeko ezininzi kakhulu, ukutofelwa igazi kufuneka lokuphelisa nya kwegazi.