I-umyalezo we sarcoidosis yaye yintoni izifo badidekile kunye syndrome Lefgrena

Lefgrena syndrome - ezihlangeneyo hilar bronchopulmonary inkqubo macala emithanjeni macala omabini. Isifo kunye obubonakala ulusu (erythema nodosum), icesina, kunye arthralgia. Ezi mpawu uphawu sarcoidosis.

Xa sifo sichaphazela amalungu ezahlukeneyo - imiphunga, udakada, iindawo nkovu. Lefgrena syndrome sarcoidosis ayihambi kwaye akukho sisifo esosulelayo. Mazingabhidaniswa kunye neenkqubo sifo oncologic kunye nesifo sephepha.

picture clinical

Sarcoidosis kuye ixesha elide isifo inqabile, kodwa namhlanje imeko utshintshile, ngezifo kwaqhenqetha ngeqondo ngokukhawuleza ehlabathini lonke. Ngokobalo manani ngaphezu kwakhe nabani na ongomnye ukuba babandezeleka syndrome Lefgrena abafazi ukusuka kwiminyaka engama-20 ukuya kwezingama-40, kodwa ke esi sifo kuza nawuphi na umntu.

Oko kunokuthi kwenzeke ngaphandle iimpawu, ngokuthe ngcembe okanye ifomu yayiyazi. iklinikhi nazimpawu ngokuqhelekileyo ukubonwa gaxa iimviwo fluorography lokuthintela. Avamise kakhulu ngamanqanaba ngamanqanaba ukuqhubeka kwesifo kunye miqondiso ilandelayo:

• dyspnea ku ngamandla;
• a bemilenze zibuthuntu esifubeni;
• intlungu phakathi ligoba ;
• ukhohlokhohlo owomileyo;
• fever eliphantsi-grade ;
• ukukhathala buthathaka;
• ukubila ngokugqithiseleyo;
• ukulahleka emnyama;
• ubuhlungu ndibanisela emva asezantsi.

Acute for sarcoidosis ekuthiwa syndrome Lefgrena, oko kukhatshwa ngokuvusa lobushushu ukuya 38-39 ° C, amalungu abe buhlungu, kolusu ngohlobo erythema, iintlungu esifubeni kwakunye nokubamba-bamba umphefumlo. Kuqhelekile ukuva xa yondele ngexesha recovery ngokupheleleyo ngaphandle kokusebenzisa unyango yabantu unyango kunye nezinye izinto.

I-umyalezo we sifo

Kude ekupheleni amayeza eyaziwa oonobangela kwesi sifo, kusenokwenzeka ukuba nimqumbise ngezo zinto zilandelayo ukuze aphuhlise:

• usuleleko, Mycobacterium tuberculosis, hepatitis C;
• izinto ezimbi yangaphandle, ukusezela uthuli metal;
• ukutshaya, nto leyo zingenangcambu unobangela, kodwa kakhulu nzima indlela sifo;
• yofuzo.

Prevention of sarcoidosis

Abagulayo syndrome Lefgrena kubalulekile ukuba ayeke ukutshaya, ukuba kukhawulezisa recovery. ixesha mfuneko ukuhlolisisa amalungu esifubeni kule minyaka-2. Kuthathelwa ingqalelo into yokuba umyalezo esi sifo ayaziwa kude kube sekupheleni, imigaqo inyathelo lothintelo ukuba kuphuhliswa. Iingcali Siyaleza musa ukudibanisa metal uthuli nakujoliso olutsha usulelo.

Lefgrena sarcoidosis syndrome elibhaqiweyo alandelayo inkqubo kwasendaweni extrapulmonary - litshitshiswe izihlunu ongama, isikhumba kunye iindawo nkovu neuropathy. Kukho ukwanda wesibeleko, subclavian, axillary neendawo inguinal. Kwezinye iimeko, le nkovu iindawo ezithile esisu ochaphazelekayo.

Bone kunye nenkqubo luvo bachatshazelwa kakhulu alufane, kodwa kunzima ukuba isifo kwenzeka. Sarcoidosis wentliziyo kwenzeka ngo-20-30% yamatyala ezi nazimpawu. kwicala lasekhohlo intliziyo kuyathotywa ngumqulu, le ukunyuka ventricle ekunene.

iimviwo Early kunye nonyango banikwa amathuba bathembele yabaneziphumo ezihle. Kwelinye icala, kukho utshintsho esiqwini lung, nto leyo ekugqibeleni kukhokelela nokukhubazeka.

Lefgrena syndrome sarcoidosis oyingozi ngobuwena

bedidekile amaninzi kunye sarcoidosis, tuberculosis ngenxa yokufana iimpawu. Oku kufuna uviwo ngokucokisekileyo, ngokuba ngoonobangela kunye nonyango ezahlukeneyo. Xa kungekho tyala ayikwazi azibandakanye self-unyango, ingakumbi ukuthatha amachiza senzelwe izigulana sephepha, oko kunokukhokelela ekufeni.

Lefgrena syndrome (a umzekelo sakudala) - oku xa imeko jikelele yomguli na uvavanyo eyanelisayo. Kukho utshintsho esikhumbeni. Angavela:

• papules kanye umonakalo;
• Chilblains lupus;
• yayenze keloid;
• lingene;
• erythema nodosum;
• SKD and CKD sarcoid Beck;
• nodes ashinyeneyo ezininzi kule inyama ongama.

ekuxilongweni

Ukuvavanywa izigulane Lefgrena syndrome kukuba ukwenza X-ray. Njengoko indlela ukuphuculwa usebenzisa Itomography ngekhompyutha. Mahanyelo hormone wegazi.

Ingxaki kunyango ukucinezela inkqubo arhabaxa. Eyona ndlela isebenzayo kukusetyenziswa corticosteroids iinyanga ezintandathu. Ukuba ichaphazela amalungu abalulekileyo kufuneka unyango hormone glucocorticosteroid.

Ngokukhawuleza ikhosi okuqhubekayo iphathwa kunye nezifundo ezimfutshane lolawulo efakwa iziyobisi ezilwa ukudumba. Kwiimeko apho uthomalaliso kungaveli, eyayibanjelwe plasmapheresis (nyulu igazi). Xa isifo kakhulu kwisigaba semiphunga zifuna nokufakelwa amalungu omzimba. Ikhosi kwesifo kunye nonyango isiphumo ubukhulu becala kakuhle, kodwa akukho mfuneko yokuba uqale inkqubo.