Zempilo, Diseases and nemibandela
Constriction .Kuma: oonobangela, iimpawu, sifo, kwaye irejimeni yonyango
Ngamanye amaxesha oomama ngokwezonyango bethe uzale abantwana abaneziphene morphological: ukunqongophala phalanges, imilenze kunye neentloko. Umama lithemba, icala yena okanye oogqirha oko kwenzekileyo umntwana wabo. Maxa wambi kuza kwetyala. Kodwa yintoni ngokwenene unobangela yokuzalwa?
definition
constriction fluid, ebizwa "ingenamthungo .Kuma" okanye "imisonto Simonara" zimele dublication amnion ngelaphu leyo esolukileyo phakathi kweendonga zesibeleko. Ngokuqhelekileyo, oko ukuwonakalisa umbungu kwaye ayibeki neengxaki ekuzaleni. Kodwa kwiimeko ezinqabileyo, kunokuphumela nemiphumela emibi.
zixhobo ifayibha, leyo kuvela esinyini ezingekazalwa - amniotic constriction. Basenokuba compress okanye ukubopha imfesane yosana eqhotyoshelwe kwezahlulo umzimba ndingekazalwa, ebangela iziphene yokuzalwa (ukusikwa izandla, iinyawo, iinzwane, okanye phalanges, maxa wambi decapitation).
izizathu
Kukho iingcamango ezimbini kutheni constriction khona fluid. Izizathu zale meko ucacisa ugqabhuka rhoqo kwiqamza .Kuma ekukhulelweni ekuqaleni. Njengoko chorion ayitshintshanga, ugrogriso kophazamiseko wophuhliso umbungu anayenza, kodwa umsonto ezivela ngenxa ikhefu, free-idada fluid. Zingakotshwa kukhatshwa ukuya umzimba iziqhamo. Ekuhambeni esakhulelwe usana lukhula, kodwa umsonto uhlala ngokufanayo njengokuba babenjalo, ngoko kukho ucinezelo le ischemia inyama kunye necrosis.
Emva kwexesha elithile, ithiyori okwesibini, njengoko wokuqala zange ukwanelisa ukungamthembi waphawula ukuba constriction .Kuma (umtya esiswini somithiyo) kuvela ngaxeshanye kunye namanye malformations bekhubazekile ezifana ngomlebe lips okanye inkalakahla emqhokrweni wengxondorha. Ezi oogqirha kuye lubonisa ukuba kukho bands ngenxa ukuphazamiseka nemithambo okanye ukuphazamiseka ejikeleza Palsy.
Enye inguqulelo kweziganeko usuleleko intrauterine, nongcungcutheko ngexesha lokukhulelwa, esini engaqhelekanga (kabini lwe isibeleko, isibeleko-ineempondo ezimbini , njalo njalo. D.), ngoCin (ukuhluleka wesibeleko), ukudumba amnion, endometritis, oligohydramnios. Kodwa akukho nanye kwezi ngcamango livunyiwe ngokuphelele.
ekuxilongweni
Kwiimeko ezininzi, zekliniki laboratory uyasilela ukuchonga constriction fluid. Iifoto ukusuka isifundo ultrasound uninformative, ekubeni ezi imisonto ezibhityileyo kakhulu. Ngokungangqalanga uyakwazi ukubona imilenze ezandisiweyo kwaye idumbile kwiindawo of ucinezelo. Ubukhulu becala ngokubanzi overdiagnosis yale ngezifo. Ngoko ke, ukuba ugqirha kurhanelwa ubukho bands fluid, abakhulelweyo ku MRI kunye 3D ultrasound.
Ngaphezu kwesiqingatha wafunyaniswa constrictions amniotic kwi ultrasound ngokuphindaphindiweyo ayikwazi ukubonwa ngenxa komsipha zabo.
izibalo
Kuxhomekeka technical sokuquqa izixhobo azalwe ngayo lo constriction .Kuma elibhaqiweyo zingaqala 1: 1200 ukuya 1:15 000 kwisizukulwana. Kukholelwa ukuba amakhulu amabini neshumi lamawaka izisu kwenzeka ngenxa yesi sizathu. Asibhozo ekhulwini kwiindawana Simonara ukugqabhuza iminwe kunye nezandla, yaye omnye ekhulwini ezilishumi - a ucinezelo le imfesane yosana. Loo ukubunjwa amaqhina intambo yosana ezikhokelela hypoxia kunye nokufa zaphambi kokubeleka ezingekazalwa.
Ngethamsanqa, uninzi zixilonga "amniotic band constriction" ayixhaswa yi imisonto zonyango okanye ezinezikhondo musa ukulimaza elibalulekileyo olungekazalwa.
ufuzo
Amathuba ukuba constrictions .Kuma kubonakala ngexesha lokukhulelwa, incinane kakhulu. Esi sifo njengelifa. Ngokuqhelekileyo, la yemfuza genomic okanye chromosomal kwenzeka symmetrically, yaye kulo mzekelo, obenosinga eqhotyoshelweyo random ngokupheleleyo. Ukuba ukukhulelwa wokuqala umntwana NS Simonara waphawula, oko akuthethi akuthethi ukuba abantwana ezilandelayo ziza owenzakeleyo. Kwakhona, oko akuthethi ukuba abazali abaye ubunzima Esibelekweni fluid band constriction, umntwana uzalelwe malformations.
imiphumela
Nangona constrictions amniotic - ayikho ngezifo akubulali, iziphumo kulo iyadanisa kakhulu. Ngenxa yokuba amaqela nga bamthiyele iindawo foetal omzimba, ukuphuhlisa nkovu kukhula. Oku kukhokelela nokudumba kunye necrosis. Emva kokuzalwa lomzimba kufuneka unqunyulwe, okanye ukuphuhlisa kuyityumza-syndrome: i obuba- wayiqokelela kwi kwesebe anesthetized, kweyela kwegazi kunye namaziko baya kuqala ityhefu usana. Oku kukhokelela ekufeni kwakhe. Kuyimfuneko ke ngoko ukuba ukususa kwesebe, ukuba sele bangazinzi. Kwaye ngokukhawuleza kangangoko kunokwenzeka.
Ukongeza, xa syndrome of constrictions amniotic ukuze misinga imilenze kunye iminwe inxalenye proximal alo mlenze. Rhoqo phakathi aba bantwana omhlophe iinzwane okanye phalanges leminwe neenzwane. Ngamanye amaxesha, ukongeza constrictions zomntwana kuvandlakanywa enye disembriogeneza ibala: inkalakahla zicandeke kunye iindevu. Kwiimeko ezinqabe kakhulu kukho ephule yomqolo kunye ukakayi yobuso, eventration amalungu esiswini, atresia le imfesane yosana.
Ukuba constriction kuchaphazela migqomo ngokusondeleyo abekwe kuyo eluswini, ke ngoko, nakweli xesha ke abunjwe hemangioma. Ithumba emva kokuzalwa kufuneka isuswe.
Ezinye izazinzulu ufumane iintambo uxhulumaniso Simonara kunye kokukhubazeka. Oku kungenxa yokuba imilenze foetal ayinakutshintshwa imisonto ifayibha, ngoko ke isibeleko nga compress unyawo olungekazalwa. Amabini ekhulwini le ngezifo yi-kabini ezimbini. Enye ingozi, nto leyo ifanele inike obstetrician - na ukuzalwa kwexesha. Le kama - zesiganeko rhoqo zokukhulelwa ezithe zenzeka kunye syndrome constrictions fluid.
unyango
Njengomgaqo, Esibelekweni sisifo asinyangeki. Xa yezonyango, kukho iimeko ebonisa apho usebenzela transvaginal okanye laparoscopy. Kodwa i ngokugqithiseleyo, njengoko amalungu abalulekileyo pinched. Kodwa ke constriction ezinqabe kakhulu fluid. Unyango ngokuqhelekileyo luqhutywa emva kokuba umntwana ezelwe.
Imicu ke dissected kwaye inqunyulwe yinxalenye lomzimba xa kuyimfuneko. Ukuphucula umgangatho wobomi zilinywe iminwe phantsi ezingalweni zakhe.
Outlook
I-ALS ubomi kunye nempilo, akholiswe ngokubanzi. Abantwana kwiimeko ezininzi akhule nokuphuhlisa ngokobudala. Qho ngonyaka imilenze baphucuka, ngoko ukulahlekelwa ziyenza njani, isandla, asezantsi ngomlenze okanye ngonyawo kunokwenzeka ukuba ukuphakamisa endaweni ngumntu. Abantwana bakhuthazwa ukuba utshintshe amazinyo njengoko bekhula. Ukuba constriction yabangela siphene minor esebenza, isiphako izithambiso lupheliswe yi iminwe transfer kunye phalanges zabo.
Xa abantu syndrome constrictions .Kuma azalwe abantwana uphilile, njengoko esi sifo ifa.
Celebrities abaye baba bands Simonara
Kuye ixesha xa abantu lomzimba umlenze bazimela emakhayeni abo lishwangusha luluntu. Ngoku ongahlala phantse akukho zithintelo, ukubamba izikhundla ezibalulekileyo zoluntu, umthambo, ukuvela kumabonwakude yaye bakwazi ukuthatha inxaxheba liphikisa ngobuhle.
abanye abantu odumileyo neentloni azalwe kunye ukusikwa bekhubazekile, kodwa ingaba oko kubangelwa constriction .Kuma - umbuzo evulekileyo.
- Carrie Bornell - actress, owazalwa ngaphandle ngesa-. Isebenza kwisiteshi kamabonwakude yabantwana. Oku kwabangela yokusabela ugalelwe phakathi ababukeli abatsha kunye nabazali babo, wanika yokukhawulezisa ukuvela uthotho lweenkqubo malunga wakuxela abantwana ngokukhubazeka kunye neempawu ezizodwa obomi aba bantu.
- Dzhim Ebbot uyiqhelile kubo bonke abalandeli baseball. Yena umphanda cishe, okt feed, ngaphandle ngebrashi ekunene. Yena umhlala-mdlalo ekupheleni kwenkulungwane yamashumi amabini, kodwa umzekelo wakhe uqhubeka ikukukhuthaza abantu abaninzi abakhubazekileyo kunye Abadlali.
- Teresa yukata - ubuhle Miss America, wazalwa ngaphandle ngesandla sasekhohlo. Ngexesha amakhuphiswano, andizange ungambathi ngengqondo, ukubonisa ukuba uyakwazi kuba yinto enobukhazikhazi ngaphandle kwiindawo zedolophu.
- UKelli Noks - model ngaphezulu ngaphandle zengalo ngasekhohlo. Ngo-2008, uye waphumelela ngokoqobo show kwi-BBC channel 3. Ukongeza kuye kolu khuphiswano ababandakanyekayo amantombazana ezisixhenxe abakhubazeke ngeendlela ezahlukeneyo.
- Nikolas Makkarti - pianist owaziwayo, owazalwa ngaphandle isandla sokunene.
- Nikolas Vuychich - yobuKristu umshumayeli Australian. Famous for kokuba azalwe ngaphandle imilenze. Yena ipapashe iincwadi zakhe aze aye nakwiisemina ehlabathini lonke njengomzekelo, ukuba bayeke nakwezona meko zinzima.
- Mark Goffeni - guitarist, owazalwa ngezandla umlenze. Wafunda ukudlala iinzwane bakhe.
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