ZempiloDiseases and nemibandela

Clinic Frederick syndrome

Frederick syndrome wavuka igama layo wokuwonga elaa komzimba Belgian, ngubani ichazwa njengendlela yindibanisela ezinqamlezayo ezipheleleyo (atrioventikulyarnoy) kwafa kunye fibrillation atrial, kwezinye iimeko - enomoya atrial. Eli nqaku lithetha Frederick syndrome: iimpawu zonyango, isifo kwaye afumane unyango lwesifo.

mechanism syndrome

Frederick syndrome ezilandelayo iindlela: ukusuka imithambo ukuya ventricles eyeka ngokupheleleyo Uhanjiso neemvakalelo; ngokunxaxha, isiphithiphithi, uvuselelo njalo nokucuthwa amaqela athile Imisonto kwezihlunu ye imithambo. Le ventricles sichulumancile yi-ntliziyo, ibekwe kwisixokelelwano uqhagamshelo okanye Uhanjiso atrioventricular.

Izizathu Frederick syndrome

Isifo kunokwenzeka emva izibhaxu somgquba zentliziyo, soloko ilandelwa ziinkqubo ukudumba, sclerotome okanye ukonakala kwi myocardium. nkqubo ziquka, umzekelo, isifo sentliziyo kobuchopho, ingakumbi ngokohlobo ezigulo ezondeleyo, iposi etsolo engabalulekanga, myocarditis, cardiomyopathy, angina sifuba kunye nabanye. Kwezi zifo imisipha intliziyo ukuphuhlisa iinkqubo sclerotic, okubangela ngokungeyomfuneko u kwizicwili, esithatha indawo iiseli zomzimba eqhelekileyo, kuvamile ukuba ungenza ukuziphatha amaza zombane. Ngoko ke, conductance iphazamisekile, kwaye kukho kwamabutho.

Yintoni na cardiogram

Ukuze uqinisekise yomguli syndrome Frederick, njengoko umthetho, ihambo electrocardiograms alawulwa. Ngaphezu koko, uphononongo olwenziwe iintsuku ngcono ukuvavanya izinga lentliziyo ngamaxesha ahlukeneyo ukuqokelela inkcazelo engakumbi.

Phambi kwesi sifo emimangweni ECG zibhalwe fibrillation okanye enomoya atrial, ngelixa umntu esempilweni kufuneka abe amazinyo. isingqisho Ventricular uba njengentsika okanye idioventricular, kwaye ngokubanzi - ethunjini nesinusovym. RR amathuba rhoqo yaye isingqisho ekunene. Inani Izinga ventricular abhalwe mali engadlulanga amaxesha 50-60 ngomzuzu. izakhiwo Ventricular zidla zikhulisiwe zikhubazekile.

Iimpawu Clinical kunye neempawu

Kuphela uncedo electrocardiogram ngokuchanileyo ukuqinisekisa isigulane Frederick syndrome. Clinic, Wayephelekwa kubomi bemihla ngemihla, nto leyo ukutsala ingqalelo loo mntu - inqabile, kodwa izinga intliziyo ekunene kunye izinga intliziyo ubuncinane 30 kwaye izihlandlo ezingaphezu kwama-60 ngomzuzu. Izinga Pulse kuncipha ngenxa yokwehla umsebenzi lokumpompa kwentliziyo. Bona, oku kungentla kukhokelela mpilo yindlala ebuchotsheni.

Izigulane becala ukukhalaza yobuthathaka, isiyezi, ukuphelelwa umoya, eziya zisiba impilo kwanasemva umthambo kancinane. Ukuba umntu akanayo ingqalelo Frederick engqondweni, ezi mpawu kuxhotyiwe, kubonakale zokuma elide imizuzwana 5-7. Ukongeza, kusenokubakho ilahleko osezingqondweni ngenxa tachycardia ventricular.

unyango

Iya isanda, oogqirha bayavuma ukuba isisombululo kuphela echanekileyo yonyango Frederick syndrome na umzila kukho pacemaker ngumntu. Oko lifakwa electrode ventricle, ezisa pulses kunye eyenziweyo ebangela yindibanisela le myocardium. Le rhoqo ucutheko bunikwa kwangaphambili kuxhomekeke imeko yomguli kunye nomsebenzi wakhe emzimbeni.

Ukongeza isantya kwaye usebenzise holinoblokatory. Le izinto ezikhethekileyo, ezifana atropine. Kutshanje, kunjalo, izicelo zabo wala ngenxa yeziphumo ebezingalindelekanga ezininzi, kuqukwa nefuthe elibi psyche yomguli, umzekelo, uphuhliso atropinovogo ngengqondo.

Ngokubanzi, unyango ixhomekeke kuzinzo hemodynamics kunye oonobangela atrioventikulyarnoy kwamabutho.

Ngenxa yoko, Frederick syndrome sinobuzaza ngokwaneleyo ukuze soyisa umsipha kwentliziyo, luphawulwa iyonke enqamlezileyo yaye kuvalwe nodibaniso fibrillation atrial.

Okwangoku, kunjalo, kunye zixilonga ezifanelekileyo ngexesha le meko sinokunyangwa, emva koko isigulane ukubuyela eqhelekileyo nokugcina indlela yabo yokuphila.

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