ZempiloAmayeza

Banti kaThixo Syndrome: Iimpawu, Treatment

"Syndrome" kusho Greek "iklasta" okanye "compound". Xa amayeza, le nkcazelo unikwa izifo ukuba abe inani elithile lemisebenzi esemqoka zingabonakali, badla ngokubonakala kunye. Ngenxa yoko, ukuhlanganiswa iimpawu kwi ukuxilongwa nga ngokuba sifo. Enye yezi ithi - Banti engqondweni.

feature

Hepato-splenic syndrome - oko ke wesibini kwigama le meko. Lubonakala yi wawandisa wesibindi kunye udakada, ngokulandelelana, ephazamisa la mabhunga. Banti engqondweni zengqondo okubangela izifo ezingapheliyo kwenkqubo hepatobiliary , kunye nezigulo nokuhamba kwegazi kwi "esangweni Vienna -. Vienna udakada"

igazi kwegazi lwemithambo esibindini kunye udakada olunika ingcaciso ngendlela ezi mizimba enxulumene nendlela ezichaphazela omnye kwi unxaxho efana Banti syndrome. Unga ukulandelela uqhagamshelwano lwemithambo phakathi kwezi imizimba.

Ekhaya Vienna - lo portal. Xa igazi lakhe iqokelelwe udakada kunye namanye amaziko kwisisu. Emva koko iwela esibindini, apho wahlambuluka iityhefu eziyingozi kwaye ke ukuba kuye kwanwenwa lonke izondlo zomzimba. Inxalenye portal iphuma splenic, lo udakada ke ngoko nolwalamano olusenyongweni kakhulu kunye wesibindi kunye neenkqubo ezikhoyo apho. Oku kuchaza isizathu, e Banti engqondweni ichaphazela isibindi kunye udakada.

Pathogenesis hepatolienal syndrome

igazi disorder kuba ngenxa licuthe le mithambo ye Kwangale portal. Kukho ngxi igazi yaye ngenxa yoko, ukwanda koxinzelelo lwegazi. Kutheni le nto isenzeka? Nazi ezinye zezizathu:

  1. ucinezelo yangaphandle Kwangale portal. Oku kwenzeka zombini ngaphakathi kwesibindi, kwaye esiqhumeni hepatoduodenal emnyango umzimba. Kulo mzekelo, bagcine iimpawu syndrome hepatolienal kunokwenzeka nezifo ezifana:
  • Ukuqina.
  • uhlobo Severe kwesibindi.
  • Thrombosis le vein Portal kunye imithambo enkulu ezikufutshane.
  • izixwexwe zesibindi ithumba Primary.
  • ngezifo wentliziyo intliziyo elungileyo.
  • Biliary izifo, nangezilonda, cysts.
  • vein thrombosis Hepatic.

2. licuthe le mithambo ye Kwangale:

  • Thrombosis le vein Portal kunye amasebe awo ezinkulu.
  • thrombosis umthambo Hepatic, okanye Budd-Chiari syndrome.

Ukongezelela kwizinto yonakalisa enokuthi abangele wawandisa wesibindi kunye udakada, oku kusengenzeka njenge yokusabela ngoyaba ukuba ukungena eziphilayo.

isigaba

Kukho izigaba ezininzi hepatolienal syndrome:

  1. Inqanaba lokuqala kunokwenzeka iminyaka embalwa. Imeko jikelele iyanelisa, kukho anemia inobulali, leukopenia kunye neutropenia. Isibindi siyongezwa, kodwa kuba udakada kakhulu ngakumbi.
  2. Inqanaba lesibini iphawulwa ukwanda okubonakalayo esibindini. Kukho iimpawu kusebenziso. Zinokuhlala iinyanga eziliqela.
  3. Isigaba sesithathu. ubude bayo - unyaka omnye. Luphawulwa nokunciphisa isibindi kunye itywina kwandisa anaemia, kukho iimpawu lwegazi, ascites, ukopha zesisu, varices esophageal.
  4. Isigaba sesine. cachexia Akumangalisi, ukudumba, kwaye ukopha iimpawu.

oonobangela

Amaninzi, syndrome Banti kaThixo ebantwaneni.

Izizathu abantwana kunye nabantu abadala ingaba ezahlukeneyo:

  • izifo njengelifa.
  • izifo ezosulelayo.
  • igazi naso hemolytic.
  • yesifo azalwa kunye ezifunyenwe ze Kwangale portal, splenic.
  • isifo Hemolytic usana.
  • utshwala Chronic.

Amaqela lweengozi ezivela kwezi mpawu

Zonke izifo ezinokubangela Banti kaThixo syndrome zingahlulwa zibe ngamaqela:

  1. isifo sisibindi kunye ezigulo ezondeleyo. Ngokuba eli qela luphawulwa iintlungu okanye imvakalelo ubunzima hypochondrium ekunene, ukuphazamiseka dyspeptic, pruritus, senyongo. Kusenokwenzeka abe hepatitis wentsholongwane egazini, qhagamshelana nezigulane ezasulelayo, ungenelelo utyando okanye ukwenzakala, butywala, iziyobisi ulwamkelo gepatoksicheskih kwiCEMIS lumngcungcuthekise esiswini, nomkhuhlane.
  2. izifo zokugcina. Igcwele phakathi kwamalungu osapho olunye okanye izalamane ezisondeleyo.
  3. Izifo ezosulelayo kunye olwaye lwamfimfitha. Zihamba kunye ukunxila, ifiva, arthralgia, kunye myalgia echazwe kakuhle.
  4. Izifo yenkqubo sentliziyo. Bona kunye tachycardia, isifo sentliziyo ischemicheskoy, ingqokelela ulwelo em- pericardial, ukwanda kunye notshintsho yoqwalaselo kwentliziyo.
  5. Izifo igazi kunye inyama lymphoid. Eli qela luphawulwa iimpawu ezifana ukudinwa, ifiva, iindawo nkovu idumbile.

symptomatology

Ukuba ugula Banti engqondweni, iimpawu ukuze ziquka:

  1. isibindi Ukwanda udakada. Ubuhlungu Ngokucofa.
  2. zokunciphisa Weight.
  3. It ephazamisa namadlala yonyango.
  4. Iingxaki kwi lokugaya.
  5. Anemia. Pallor kunye nesikhumba owomileyo.
  6. olwenzeka kunokwenzeka kolwelo kwi kwisisu.
  7. Ubuhlungu bemisipha.
  8. Yellowing lweenwebu protein yamehlo.
  9. Tachycardia, uphelelwa umoya.
  10. izikhonkwane nkum ilahleko iinwele.

Moshilongo kuyimfuneko ukuba ekuhlolweni, kwaye uhlalutyo olubanzi imizimba - isifo.

ekuxilongweni

Ukuba ngaba wehlelwa zezi mpawu zingasentla uxilongo mahluko of hepatomegaly kunye hepatolienal syndrome. Ukuze wenze oku, kufuneka asebenzise uluhlu lwemisebenzi. Elinye lamanqaku yokuqala - uhlalutyo jikelele igazi kunye nophando layo ezinto eziphilayo. Ukuze ubone isizathu sokuba kwakukho Banti engqondweni, uxilongo umahluko kukho unxibelelwano. Izilingo:

  • Sonography wesibindi, udakada, nenyongo isinyi, neempahla esiswini.
  • Itomography ngekhompyutha.
  • Ukukrwaqula kwesibindi kunye udakada.
  • iimviwo X-ray le duodenum.
  • Laparoscopy.
  • Punktsionalnaya biopsy kwesibindi kunye udakada.
  • Uviwo lwe umongo kunye zamanzi.

Kungoku nje isayensi Kwakumi ngxi kwaye sanda olawulo lokufunyaniswa uhlalutyo ezifana imeko njengoko Banti engqondweni. diagnosis umehluko kunye nesifo engundoqo kunye nemeko kwezonyango kwesibindi ukuba ikhona, ngumsebenzi ophambili.

Treatment kunye iingxaki sifo

Njengomgaqo, unyango syndrome hepatolienal kukuchonga inkqubo isifo bha ngonyango. Asinto sisifo elizimeleyo. Ukuba ngaba une-"syndrome Banti kaThixo", unyango kufuneka agcine gastroenterologist. Kulo mzekelo, sebenzisa gepatoprotektory, antivirals, iihomoni kunye neevithamini. Kwimeko nganye, ukuze abe indlela ngamnye, kuthathelwa ingqalelo umyalezo kwesi sifo.

Ukuba akusibonanga eso sifo yaye akukho unyango, i-ALS inokuba yintlekele. Iingxaki kule syndrome - i kwesibindi, isibindi vein thrombosis, ukudumba esinyini inyongo, izifo igazi. Kwiimeko ezinjalo, yokususa ziqwempu isibindi kunye udakada okanye abohlukeneyo kunye kwegazi.

Inxaxheba kwinqanaba lokuqala, izigulane bayakwazi ukusebenza kwaye ukumelana umsebenzi kancinane. Kwixesha elizayo, kunye ukuvuthuluka meko isigulane enesiphene esithile.

ukuvimbela

Ukuze ukuba ukuphoswa isiqalo nophuhliso ngezifo, kufuneka:

  • igazi nomchamo iimvavanyo rhoqo.
  • ekuhlolweni ngexesha elifanelekileyo, ingakumbi xa usengozini.
  • Uthintelo hepatolienal syndrome ngokuyintloko kuquka ukulwa oonobangela libangele isifo sesibindi kunye udakada.
  • Qiniseka ukugcina ukutya echanekileyo kutya eziqulathe anenani elifunekayo amafutha, iiprotheni kunye carbohydrate kwaye, kakade, iivithamini.
  • Musa kakubi utywala, icuba siphile ubomi obusempilweni.

Akukho zifo engeyongozi, ingakumbi ukuba babalise amalungu omzimba abalulekileyo afana isibindi kunye udakada. Ukuba isigulo kwangethuba iingxaki, kwaye ngoko ke unyango olufanelekileyo uyakwazi ukunika iziphumo olusebenzayo.

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