Zempilo, Diseases and nemibandela
Aortoarteriit nonspecific: Iimpawu kunye Indlela Treatment
Okwangoku, kukho inani elikhulu izifo enokuchaphazela amalungu ezahlukeneyo neenkqubo zomzimba. Ke phakathi kwabo kukho abo bakhetha ukuba ukhethe besini esithile. Kweli nqaku, senza aqhelane enye yezi zifo - na aortoarteriit nonspecific, nto leyo edla unale wesini ababhinqileyo, kunye nabantu abatsha. Esi sifo ngokuqhelekileyo sifo kumazwe Asia. Makhe sijonge izinto zayo, iimpawu, yaye kwangaxeshanye xoxa ukuba unako ukumelana nale ngezifo.
Kakuhle eli sifo
aortoarteriit Nonspecific sisifo samathambo apho kukho indawo ilahleko engaphakathi kwemithambo kunye amasebe awo. Ukuba inkqubo yokukrala iqhuba, udonga ukuqina semithambo, smooth umaleko kwezihlunu iqalisa ukuba ndiludilize kwaye kwafakwa kwizicwili, yaye igazi nempahla kuvela granulomas equlathe weseli enkulu.
Ngenxa imithambo yegazi iinkqubo ezinjalo ukwandisa kunye uPienaar kuphuhlisa kwemithambo. Ukuba le nkqubo akayeki, ngoko iphelile babebona ukulahla imicu elastic of egudileyo ijwabu kwezihlunu. Qala kubandezeleka amalungu kunye izicwili ngenxa yokumpompoza kwegazi kakuhle. Kwinkqubo ngamazwe yokuhlelwa kwezifo, isifo nganye ikhowudi yayo, hayi ngaphandle aortoarteriit nonspecific. ICD M31.4 yanikezelwa kuye ikhowudi (aortic kwinqugwala syndrome).
Ezibangela isifo
Ukuza kuthi ga ngoku, oonobangela ukuba bawaphikise uphuhliso kwesi sifo, kwaye iye ayasekwa. abaphandi abaninzi abo benza lo mba, banengcinga ukuba akukho indima yokugqibela kule edlalwe zizifo, akhokelela immunodeficiency ithi. Loo uluvo wasekwa ngenxa yokuba aortoarteriit non-ngqo unxulunyaniswa kunye nezifo, ezo zisekelwe ukuphazamiseka omzimba.
Okwangoku, kukho iqela iinzululwazi nabavumayo ngelihambisana kwithiyori yophuhliso isifo samathambo. Ubungqina leyo ekufumanekeni kwezigulane kunye izilwa-plasma antiaortalnyh.
Sinokuthi indlela lwesifo samathambo zingangqinwa, kodwa nokuba ngowona, okanye ukuphendula kwinkqubo yokukrala - bathi kangaka nzima kude.
nokubekwa kwezifo
Aortoarteriit nonspecific unokuba iintlobo ezahlukileyo ngokuxhomekeke kwindawo ochaphazelekayo:
- Uhlobo lokuqala - kule meko wambetha kuphela arch amancinci amasebe aortic ukuba bandise kuwo.
- Xa Uhlobo lwesibini Umthambo nachaphazelekayo thoracic kunye esiswini.
- Uhlobo lwesithathu - abachaphazelekayo arch aortic kunye thoracic kunye esiswini.
- Okwesine luphawulwa izitshanguba kwemithambo miphungeni.
Ngokuba konke scheme okanye ukuphuhlisa aortoarteriit nonspecific (disease Takayasu kaThixo), ukukhubazeka esongela ukugula kakhulu kunene. Ingakumbi xa ukuxilongwa kwexesha.
symptomatology kwesifo
Aortoarteriit iimpawu nonspecific yahlukile, kuxhomekeke kuhlobo kwesi sifo. isifo Takayasu abe kwisigaba ezingapheliyo kunye bukhali.
Isigaba nokoyika esi sifo eyaboniswa mpawu zilandelayo:
- fatigue jikelele.
- Ngexesha umthambo, iintlungu imisipha namalungu.
- Kubonakala ufunga haemorrhagic.
- Ukuphuhlisa erythema nodosum.
- Ukwandisa imida intliziyo.
- Kubonakala bambombozela iSystolic ubala ukuzala.
- iimeko Rare ubuhlungu esiswini.
- Ukuba siphatha iimvavanyo elebhu, babonisa anaemia ngomlinganiselo, ubukho C-izidubuli protini.
Kaninzi, ngokubonakala iimpawu ezifana nomkhuhlane -, "TB" "isifo samathambo" okanye "nokudumba." Oku, ngelishwa, kwenzeka ngo-95% yamatyala.
Inkqubela kweqonga ezingapheliyo zesi sifo
Ukuba zigaba zokuqala zesi sifo musa ukuthatha amanyathelo asebenzayo ukunyanga kuyo, ngezifo kungekudala uba ezingapheliyo. Symptomatology yahlukile sele evela kuloo kwisigaba ludlule:
- Ngokoqobo akukho sazi icala elinye, kwaye maxa wambi zombini.
- Izigulane ezikhala intlungu eziphelweni, ukuba ukwandisa umthwalo ziyanyuswa kuphela.
- Izandla fehle, nzima ukuba abantu ukubamba izinto.
- Amaxesha amaninzi iba unesiyezi, leyo kungakhokelela ekulahlekeni sezingqondweni.
- Xa utyelela zamehlo kubonakele utshintsho fundus.
- Ekubeni le nqubo idla kwemithambo yenhliziyo, oko waphawula kukuhlaselwa kobuchopho.
- Ngenxa ekubulaleni aorta esiswini baqalise zezintso.
- zizigulo zemithambo kubonakaliswa njengoko ingqalelo kakuhle kwaye inkumbulo, umthamo ukusebenza.
- Ukuba luvo optic lo nawo uye uchaphazeleke, ngoko ubunzima umbono, umbono kabini livela, babe ziimfama kwiliso mnye.
- Ukubandakanyeka kwe-pulmonary ekhokelela kuphuhliso ukuphelelwa umoya, iintlungu esifubeni.
- Bayekeni amalungu izandla.
- Xa nonspecific inkqubo andise aortoarteriit iqala kunye imithambo ephambili, nto leyo kukhokelela ekwandeni uxinzelelo lwegazi ngenxa licuthe imithambo yegazi.
Ngokwesiqhelo, isigaba zale sifo uba ezingapheliyo iminyaka 6-8. Izigulane kufuneka uqaphele ukuba sisoloko bathuthunjiswe ubuthathaka, intloko ebuhlungu, iintlungu ngethuba kwemithambo ezinkulu, uququzelelo kakuhle kunye nememori. Kufuneka ukuba bangenele uviwo olupheleleyo ukuze kuqinisekiswe ukuxilongwa.
uphethwe
Ukuba kukho urhano of aortoarteriit non-ngqo, isigulo kwangethuba kubaluleke kakhulu. Esi sifo ingqalelo ngoogqirha, ukuba kukho ezi mpawu zilandelayo:
- Ukuba ngaba kukho umahluko omkhulu uxinzelelo lwegazi ezandleni ezahlukeneyo.
- Pulse elibuthathaka kakhulu okanye akukho ubonwe.
- Kukho claudication uveza.
- Xa ukumamela ingxolo iqatshelwe aorta.
- Iimviwo kutyhilwa Umthambo exineneyo.
- Insufficiency ye ivalve aortic.
- ukwanda ziqhubeke koxinzelelo.
- ESR luyanda ngasizathu sithile.
Okokugqibela, ukuze gciwane izifundo zilandelayo:
- Uhlalutyo ezinto wegazi kubonisa makhwiniba igazi ukuba uphawu kwesi sifo.
- Ultrasound Ukuhlolisisa iimpahla ukuhlola imeko yabo kunye isantya sokuqukuqela kwegazi.
- Angiography ne Inaliti umahluko ibhaqa umfutho constriction.
- Chest X-ray ekufumaneni indawo izitshanguba le aorta kunye pulmonary.
- Echocardiography ukuvavanya ukusebenza kwentliziyo.
- Ngu electroencephalography uyakwazi ukubona yokuphazamiseka imithambo yegazi lobuchopho.
Ngenxa yoko, ngenxa yaso nasiphi na isifo, kuquka ezifana aortoarteriit nonspecific, imbali yezonyango iqala phando epheleleyo, leyo ijolise alungise isifo.
diagnosis umehluko
Kubaluleke kakhulu ukuba kuyokufunyaniswa isifo ukuze ukohlula aortoarteriit mgaqweni iziphene kwinkqubo olujikeleza kunye thromboembolism. Kuba yokugqibela iphawulwa ikhosi nokoyika ukuma eli ihlwili legazi em- imisipha yenhliziyo.
Into ebalulekileyo kukuba non-ngqo kuchaphazela aortoarteriit iqela neempahla, ngelilixa mgaqweni iziphene ubunzima imithambo ezithile.
Ukuba uxhomekeke kwi lwegazi isifo renovascular, kubalulekile ukukhumbula ukuba ukuphuhlisa izitya yegazi kunye sezintso. Ukuba aortoarteriit nonspecific senzeka kakhulu kwabasetyhini abasebatsha, yamafutha kuchaphazela namadoda amakhulu.
Kuphela uviwo olupheleleyo zeengcali abaqeqeshiweyo kuya kunceda kwenza uxilongo kunye ukuqalisa unyango olusebenzayo.
syndromes Clinical phakathi kwegazi
Ngenxa yokuba kule ngezifo kungachaphazela amacandelo ahlukeneyo impahla kubonelela igazi enyama yangaphakathi, kunokwenzeka ukuba ukwaba syndromes ezininzi clinical:
- deficiency syndrome yokumpompoza kwegazi yoluvo. Ngelo xesha kukho buhlu- iingalo kunye imvakalelo antsi kwi iminwe. Ukuba usindwa kwemithambo vertebral, iintlungu phaya emva apho.
- Senhliziyo syndrome - linxulunyaniswa kuphuhliso ejikeleza izibambiso. Ngaba ukuhlola iimpawu myocarditis, ischemia.
- Ukuba arch aortic ezichaphazelekayo, okhulayo cerebrovascular syndrome. Kuboniswa yintloko, kunciphise umbono, ukuphazamiseka ejikeleza lobuchopho.
- Besisu syndrome kuboniswa iintlungu esiswini, leyo paroxysmal kwindalo. Oku kubonisa akuqhelekanga xa izitshanguba le aorta esiswini.
- Lwegazi syndrome - ivela njenge ngenxa izitshanguba kwemithambo sezintso.
therapy
Ukuba une unyango "aortoarteriit nonspecific" lenzelwe ukuba:
- nempembelelo ebalulekileyo ugqaliselo ukudumba, mhlawumbi ngokunciphisa ukuba ubuncinane.
- Ukulwa iingxaki kobuchopho.
- Susa kubonakaliswa lwegazi.
Kuthekani ukuba umntu abe aortoarteriit non-ngqo? Uxilongo baqhuba iimvavanyo wathuma, umsebenzi ingcali - ukwakha irejimeni yonyango. Therapy babe ngolu hlobo lulandelayo:
- Imithi.
- Surgery.
Qwalasela ubungqina kunye iimpawu ukhetho ngalunye.
yonyango ngamachiza
Yemithi aortoarteriit xa kuqwalaselwa ubuzaza imeko yomguli kunye iimpawu nokuqukuqela inkqubo arhabaxa. Amachiza zilandelayo emiselweyo kakhulu rhoqo:
- "Prednisolone" xa isixa-mali ka-1-2 mg kwekilogram ubunzima isiguli ngasinye. Ukwamkelwa lwenziwa iinyanga 1-2.
- Ukuba ukudumba inophawu obuthathaka, iyaboniswa ukufumana aminohinolinovogo amachiza, umzekelo, "wenze Ichibi" ku 0.25 g
- unyango Basic isekelwe phezu ulwamkelo "methotrexate". Idosi ichanekile 7-10 mg square indawo umphezulu ngomzimba imitha nganye. Reception - kanye ngeveki.
- arhente Auxiliary ke anticoagulants, ezesifuba iziyobisi kuthoba uxinzelelo lwegazi.
Unyango ngamachiza inophawu elide, ukuba akukho uphuculo okanye kukho uphazamiseko okuphawulekayo amalungu omzimba, ingqondo, kucetyiswa ukuba ukubhenela ungenelelo yotyando.
unyango ngotyando
Ukuba zonyango angqingqwa awakuncedi, yaye le meko uya kufumana kuphela mandundu, ukuba luhlaza kukhathalelo yotyando. Surgery kunceda ukubuyisela igazi kuqukuqela Amalungu nezihlunu. Kodwa ke kufuneka kukhunjulwe ukuba inkqubo yokukrala kufuneka kumiswe ngaphambi uqhaqho. Kukho iindlela ezininzi olu hlobo unyango:
- Endarterectomy. Oku kwenziwa phambi angawodwa segmental occlusion kwemithambo, ibaleke ngqo ukusuka aorta.
- Agnioplastika wenziwe ukuba kukho utshintsho izitya ngabanye nezintso.
- Esa yokumilisela lwenziwa usebenzisa afakelweyo zokwenziwa nemithambo. ukungenelela olunjalo ngempumelelo izilonda ezininzi nemithambo.
Emva kwethuba kwimo kotyando kubalulekile, ngokuthotyelwa kwezo ngcebiso kugqirha.
Iingcebiso iziguli
Siye safumanisa ukuba yintoni na aortoarteriit iimpawu nonspecific kunye nonyango nabo ingqalelo, kodwa ke isigulane ibaluleke ngokufanayo ukubona zikhokelo zilandelayo:
- isigulane ngasinye kufuneka bazi ukuba unyango lwesi sifo kufuna ixesha kunye nokugcina lokuqeshwa zonke kagqirha.
- Kuyimfuneko ukuba zilandele ngqo le nkqubo kwaye umthamo amayeza oye wacebisa ugqirha.
- Ekubeni kuthathelwe izixa ezikhulu iziyobisi, kukho ingozi yokuba iziphumo ezahlukeneyo ezibi ngexesha unyango. Ukunciphisa kubo, kuyimfuneko ukuba bangenele iimviwo rhoqo kunye neemvavanyo yokupasa.
- Xa ukuvuthuluka imfuneko ukwazisa specialist.
Ukuba ngqo ezi ngcebiso, uthomalaliso esi sifo iya kuba nempumelelo ngakumbi.
Le abane ukuba izigulane
Ngelishwa, ukuba balahle aortoarteritis non-ngqo akunakwenzeka, kodwa ukuba zonke iingcebiso kagqirha kunye unyango olusebenzayo onokufikelela uxolelo. Oku kuya kuvumela izigulane ukuba nenxaxheba imisebenzi yesiqhelo kwaye uzive iintlungu.
Nokulunga unyango kuxhomekeke ebukhulwini ukudumba kunye nobukho iingxaki, kwaye liyachatshazelwa nokuchaneka kunye nesantya kokuxilongwa. Ngoko ke, ngenxa yokuba unyango iyancumisa, kuyimfuneko ukuba ukubona sifo isaqala.
amanyathelo ezizodwa othintelo ezinokunikezelwa.
Nasiphi na isifo ifuna indlela esinzulu, ekuphela kwendlela ukufikelela uphuculo okanye litshitshiswe sifo. Thatha Ukunyamekela impilo yakho uze kuhlolwa rhoqo - ukuze ukwazi ukubona ezingaqhelekanga kusekwangoko kwaye ukukhetha unyango olusebenzayo.
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