Syndrome elongate slot QT: inkcazelo, izinto kunokwenzeka kunye neempawu unyango

Impilo Human - icandelo engundoqo eziqhelekileyo kunye nomgangatho wobomi. Kodwa ke akusoloko uziva uphilile. Iingxaki ngenxa yezizathu ezahlukeneyo Vuka, kunye nokubaluleka kwazo nazo zinokuba nomahluko. Umzekelo, ingqele eqhelekileyo akuthethi ukuba iinkxalabo abantu, ukuba uyazinyanga ngokukhawuleza yaye oko kubangela umonakalo omkhulu kakhulu empilweni jikelele. Kodwa xa kungavela enyama yangaphakathi iingxaki, oko kuyingozi kakhulu ubomi umphelo ngokonakalisa kakuhle-ntle yethu.

Kutshanje, baninzi abantu bekhalaza neengxaki zentliziyo kunye amaninzi oko izifo eziqhelekileyo ekulula ukuba ukunyanga nokuxilonga. Kodwa kukho amaxesha xa isigulane ibhaqe elide QT syndrome. Xa amayeza, lo gama kubonisa okanye imeko efumaneke ngayo loo mntu, kunye ukwanda ngexesha ECG ingxenye lekhefu. Kwaye kule syndrome yayanyaniswa zobude kuphela abangaphezu kwama-55 ms ukusuka amaxabiso eziqhelekileyo. Enanikade xa sifo iphuhlisa, indices zokutenxa bekhefu ibe ngaphezu kwama-440 ms.

kubonakaliswa

Kwiimeko ezininzi, isifo yomguli kukuba nazimpawu kunye self-fumanisa kuba nzima. Ngokubanzi, abantu kwesi sifo yephule repolarization kunye depolarization ngenxa yeenguqu macala innervation kwentliziyo. Isaziso kunokwenzeka kuphela ekuhambeni zophando, ngenxa yokuba izixhobo iintlobo ezahlukeneyo. Eyona nto iphambili negalelo kule meko ukungazinzi yombane imisipha yenhliziyo.

Abantu abaye babe elongate slot QT syndrome kunyango angasebenzi okanye ukungabikho wayo ukuphuhlisa ventricular fibrillation okanye ventricular tachycardia. Ezi iingxaki eziyingozi kakhulu ukuba ubomi izigulane ezininzi ubuthwale nangeendleko zikarhulumente jikelele. Ngoko ke, ukuba ukrokrela phambi sifo kufuneka ngoko nangoko kukukhathalela impilo yakho, kungenjalo ukuze nemiphumo emibi. Ukongeza, iingxaki esi sifo unzulu. Abakwazi nje kungakhokelela kakuhle kunye Ukonakala karhulumente yomguli jikelele lezempilo, kodwa ebulalayo.

iintlobo

Xa amayeza uye wafunda elide ukutenxa enjalo, kwaye kule minyaka izazinzulu ukulawula ukufunda ngalo ngakumbi. Isifo yahlulwe iintlobo ezimbini, ezizezi, ezifunyenwe kwaye iziphene elide QT syndrome lokuphumla. Misela ukuba loluphi uhlobo nomonde, kuphela indlela kuphando. Xa izifo bekhubazekile yeyona ngxaki kukusilela ikhowudi yezofuzo. Xa oyithengayo kuphuhliso sifo achaphazelekayo imiba eyahlukeneyo.

imilo

Kwakhona cell ukuba iindidi ezithile sifo:

• ifomu angasebenzi. Lubonakala yi izikhombisi eziqhelekileyo lekhefu ngethuba loviwo, kwaye uhlaselo lokuqala syncope kukho ukufa ngequbuliso.
• Uhlaselo bokugcinwa syncope, kodwa QT bekhefu ivuselelwe ngexesha lokuhlolwa.
• Zobude bodwa lokuphumla kwaye kubonakala kwimbali.
• Syncope kuhamba isalathisi zobude QT, izinga 440 ms nangaphezulu kunene.

izizathu

izinto ezininzi ibenefuthe kuphuhliso kwesi sifo. Umzekelo, ukuba uqala ukuphuhlisa ngenxa yezifo amafa kuquka syndrome P-U. Kulo mzekelo rhoqo ekulahlekeni uxhuzula ingqiqo okunene kukhokelela kuphuhliso sifo. Kwakhona, E-P-A syndrome, ukuba isigulane unalo ukungeva naso. Yintoni isizathu yindibaniselwano ezinjalo iimpawu kwaye ichukumisa njani uphuhliso sifo, izazinzulu ziye zafumanisa ukuba ayiphumelelanga ukuza kuthi ga ngoku. Kwakhona, gene guquko kunokubangela uphuhliso sifo. Oku ngoyena nobangela uphambili yesifo awazalwa enaso, kodwa kwezinye iimeko asiyi kuba kwaoko, kwaye ibe omdala, emva ukubandezeleka ntshikilelo. Ngokuqhelekileyo le ngxaki kunye Yindibanisela iiproteni sodium kunye potassium namajelo izinto axhokonxe elongate QT interval syndrome. Isizathu unakho kulala iziphumo ebezingalindelekanga zamayeza athile. Uninzi usongo ke antibiotics enamandla ukuba isigulane ukuze ukunyanga ezinye izifo.

Inokubangela isifo okanye ukutya pathways ukunciphisa calories ekutyeni. Ukuncipha komzimba kwezi meko engabonakaliswa nje kuphela entliziyweni. Ngoko ke, ukudla okunjalo ingcono ukuthethana kunye nogqirha kwaye bagcinwa phantsi kolawulo lwakhe. Nokufa kunokubangela iingxaki izifo ezithile sentliziyo ezifana nesifo sentliziyo okanye mitral valve prolapse. maxa wambi syndrome ngenxa ezimbi CNS kunye DYSTONIA nemithambo kunye nezinye ukuphazamiseka kwenkqubo yawo luvo.

iimpawu

Kukho iimpawu ezithile ezibonisa ukuba isigulana ekhoyo QT elide syndrome. Iimpawu zesi sifo zibandakanya:

• Ukulahleka lokuqonda ihlale imizuzu embalwa ukuya kwikota yeyure. Kwezinye iimeko, uhlaselo ingahlala imizuzu engamashumi amabini.
• Unditsho kwiimeko yababhali ezifana sokuwa ngembonakalo, kodwa iinkqubo engabangela ukuba zahluke kakhulu.
• ubuthathaka ngesiquphe emzimbeni, sikhatshwe mnyama amehlo.
• Iyangongoza kwanaxa kungekho msebenzi emzimbeni okanye emoyeni.
• iintlungu esifubeni yendalo eyahlukileyo, baqhubeka ngexesha nentliziyo fast, kwakunye lokuhamba nabo besifa okanye isiyezi kunye ndindisholo izandla neenyawo.

ekuxilongweni

Amaxesha amaninzi, elide QT syndrome, abantwana ingakumbi, akukho mpawu. Kulo meko, isiguli Sinokungaziva siphilile ngokupheleleyo kwaye ngakuye ngephanyazo ngesiquphe. Ngoko ke, ukuba umntu usemngciphekweni isifo, kufuneka rhoqo axilongwe ngugqirha ukuba naziphi na yokuphuhlisa sifo. Ukufumanisa isifo, iyeza mihla isebenzisa iindlela eziliqela.

Ukuba kukho urhano lokuba iingxaki elide QT zempilo syndrome nomonde uze ubonise ngokucacileyo oku, lo electrocardiogram - kufundwa ibalulekileyo ebonisa izifo. Ngaye phakathi uhlaselo, iyunithi iza kubonisa iimpawu tachycardia ventricular, adlulele ventricular fibrillation. Le ndlela yeyona ndlela iphambili esi sifo nokuzimisela.

Kukho esinye isifundo ebonisa ukuba side interval syndrome QT. Oku kwenziwe ngexesha lasemini. Ngoko ke, ibizwa ngokuba esweni ECG. Uphononongo ivumela ukulungisa umsebenzi kwentliziyo yomguli ngeli thuba. Ukuba isixhobo sakhe ninamathele umzimba esincinane ubhala ubungqina intliziyo, yaye emva kokuba ukususwa kwaso, ingcaphephe inxaxheba ezama kwisixhobo idatha. Amvumela ukuba ukufumanisa ukuba isiguli bradycardia kakhulu engqongqo, nokuba tshintsho morphology lencinibakazi T, kwakunye nokuba kukho nto kukwaphula iinkqubo repolarization engabalulekanga kwaye ventricular ibetha ngaphambi kwexesha.

unyango

Ukuba isigulane iye yachongwa QT elide syndrome, unyango kufuneka ibe ebanzi kwaye kufanelekile, ngokuba nde kwendlela kuphela iyaluthintela uphuhliso iingxaki ezinobungozi empilweni kwaye baphathe isiphumo ebulalayo.

unyango ngamachiza

Isifo sephepha sinokunyangeka kusetyenziswa amachiza antiarrhythmic. indlela yonyango Kakuhle okhethiweyo akazukuphelisa iimpawu zesi sifo, kodwa ixesha elide ukuze uzinzise nemithambo yegazi. Le yenye yeendlela ukuba ndiphilise syndrome naso interval evuthelweyo QT LQTS.

unyango ngotyando

Ukuba isigulana kukho ingozi ingozi ebomini ngenxa arrhythmias kwesi sifo, iingcali Sicebisa betyale ipacemaker. umsebenzi yakhe ukubuyisela amaza izishunqulelo kwemisipha kwentliziyo. yesilungu liqulunqe isixhobo okhethekileyo, leyo iza kucacisa unxaxho zophendlo lwezifo kwentliziyo. Isigulo ingabangelwa evela ngaphandle. Ngethuba umthambo, umzekelo, isixhobo ngeke aphendule. Kodwa ukuba pulses ziya kuthwalwa umlinganiswa lwezidumbu, oko normalizes umsebenzi umzimba.

Utyando kwesi sifo ezifana side QT syndrome lokuphumla, ilula kwaye ekhuselekileyo ngokwaneleyo. Ntliziyo Iqinisekile ukuya ekhohlo izihlunu ezinkulu pectoralis. Ukususela kulo electrode ukuba oogqirha lukhuselwe kwindawo elifunekayo, ewakhokela Kusenjalo subclavian. Izixhobo anokuthi alungi-lungiswe yi uhlelo. Ngalo uyakwazi ukutshintsha i parameters kwayo yokulola wentliziyo, kuxhomekeka iimpawu zomntu yesigulana. Amnike iya kwenzeka ngexesha ngalinye xa umsebenzi izihlunu entliziyweni kuya kuhamba ngaphaya parameters ekhankanyiweyo.

isiphelo

Esi sifo akusoloko kusenzeka ukuxilonga kuba akufane amazwi abonisa. Kodwa kwangaxeshanye isoyikiso empilweni yomguli likhulu kakhulu. Ngoko ke, ukuba kukho na umngcipheko kancane livela, kufuneka kubanjwa rhoqo nokuhlola nokubonisana neengcali. Ukuba uphethwe kuqinisekiswa, kufuneka ibe unyango olunzulu ngokupheleleyo kwesi sifo, kuba oko kunokukhokelela ekufeni.