Zempilo, Diseases and nemibandela
Chorea - a ... Chorea ebantwaneni. chorea rheumatism
Chorea - a ngezifo-luvo. Libhekisela iintlobo hyperkinetic. Isifo sikhatshwa iingxaki kunye ezalathelwe uphuhliso palsy subcortical. Kunokuba ukuchonga yeempawu: an episodic, nanjongo twitching umbhodamo izandla neenyawo, maxa wambi yomqeshi. Kumanqanaba kamva kukho abakhubazeke ngengqondo kunye ngokwasengqondweni, iingxaki uququzelelo, nokuzeyisa-nkonzo. Abantwana chorea nto bayikholelwayo rhoqo umsebenzi eqhelekileyo landa. Enyanisweni, xa imiqondiso yokuqala sisifo kufuneka ufune uncedo abaqeqeshiweyo.
Igama elithi "chorea"
Eli gama lisetyenziswa kwiimeko ezimbini. Kusenokuba ukonakala isifo elizimeleyo, engena kweli qela (umz, chorea a Huntington encinane okanye chorea). Kwakhona lisetyenziswa ukuchaza syndromes ezithile zisenzeka xa iintlobo ezahlukeneyo izifo. Igama elithi "chorea" lisuka ulwimi isiGrike, apho kubonisiweyo yi uhlobo oluthile umdaniso. Oku kuchaza iimpawu yokuqala, leyo azibonakalisa kwezindawo, unganxibelelananga apha, ayinako, iintshukumo ngokukhawuleza komboko yesiqephu. Ukuziphatha kwe isigulana ngokwenene mbulo, umdaniso bahlupheke. Kudala-dala ebizwa chorea "umdaniso St. Vitus kaThixo." Eli gama edibene iinkolelo yamandulo St. Vitus, nto leyo ngenkuthalo ubuKrestu, awusebenzeleyo wathuthunjiswa ngamajoni aseRoma. Emva kokufa kwakhe yaba banentsomi ethandwayo ukuba umntu enze into umdaniso esebenzayo engeenxa zonke engcwabeni lakhe lokuzalwa kwakhe, yena uya kufumana isigxina vivacity namandla ka wonke unyaka.
izizathu
Ubangelwa sifo usenokuba imvelaphi ezahlukeneyo, kodwa ubukhulu becala chorea enze izinto zofuzo okanye ukuphazamiseka yemfuza.
chorea azixhaphakanga, obangelwa uhlobo ezosulelayo izifo ezifana -TB meningitis, kobuchopho wentsholongwane egazini, neurosyphilis, isifo Lyme, unkonkonko. Ukwenzeka kwe chorea esinxulunyaniswa ne ongaboniyo pathways (ukuba kukho isifo Fabry kaThixo, hyperglycemia, hyperthyroidism, okanye isifo Wilson kaThixo), intoxications (ityhefu yomlomo zokucwangcisa, imetyhuri, lithium, digoxin, neuroleptics, levodopa), ezimbi samathambo (ezifana antiphospholipid syndrome , zomzimba systemic lupus, multiple). Phakathi sezizathu ukuba bawaphikise elivela kuzo izifo, oogqirha ebizwa kwakhona izakhiwo ingqondo umonakalo. Ezi ziquka ithumba Ukwakheka, hypoxic Encephalopathy, ukwenzakala ebuchotsheni esibuhlungu, kwamalungu omzimba.
iimpawu Common
Chorea - sisifo kuziveza random, umbhodamo, iintshukumo emzimbeni elifutshane. Kwezinye iimeko, le kungaba kuthathwa njengento eqhelekileyo, eyaneleyo, okufana umntu esempilweni, into ukuxhala. Eka van'wana, ziyafana ngokweemvakalelo, umdaniso kungalawuleki. Ezixhuzuxhuzulayo ukudideka ingaba olulodwa okanye ezimbini-kabini, kodwa babe bengenazo ubuncinane uhlobo ezinye nongqamaniso.
Kuxhomekeka koko wafumana uhlobo ngezifo, bahlule iimpawu chorea. Ukuba umntu abuthethe kancinane hyperkinesis trochaic, ngoko ukuziphatha lwakhe wabona motor inkxalabo minor, ephelekwa motor disinhibition, landa nesithukuthezi, ngenxa nezindlela ezithile, ukujikeleza, izijekulo ezingafanelekanga.
Iifom enomahluko ibonakaliswe iintshukumo chorea bokuhlala "-yo yo '. kakhulu lwe hyperkinesis trochaic sigqwethe isindululo ukuhamba, intetho kunye nembonakalo yobuso. iqinelwa yomguli asinto nje engaqhelekanga, kodwa kwezinye ngomlinganiselo "upopayi". Chorea, iimpawu zazo nzima kakhulu, akavumeli nokuba enze ezinye iintshukumo. Ezinesifo kakhulu axhomekeke kwindalo lwabo, njengoko kuyo akasuki kwaye ukulungiselela wena ebomini ngokupheleleyo.
chorea Huntington kaThixo
Le leengxaki esizibonakalisa kwiimeko ezininzi phakathi kweminyaka eli-35 ukuya kwezingama-45. Chorea, iimpawu leyo, ukongeza hyperkinetic eqhelekileyo, athwale iingxaki ubuntu ngakumbi kunye ne-dementia (ukuhla Ubukrelekrele) uvela kancinane, ngamanye amaxesha kunzima ukufumana mzuzu xa waqalisa ukuhluma. Iintshukumo yokuqala enogonyamelo ngokuqhelekileyo kwenzeka ebusweni. Bangakwazi mazingabhidaniswa automatisms motor random (kulo ulwimi, elibukhali, equmbile, wayimunca imilebe, emlonyeni lokuvula). Ukuqhubela phambili kwesifo esibonakaliswa kuphuhliso hyperkinetic yomqeshi kunye yesiqephu. uhlobo ezimandundu luphawulwa abanezithintelo zentetho, inkumbulo, inkqubo yokuginya, inqanaba self-nkonzo kwaye iphela nge sengqondo esixhalabisayo. Qala ngokuba chorea Huntington xa kukho ukuphazamiseka kwengqondo ngohlobo ukuphazamiseka hallucinatory-paranoid, ngokwenene kunye nokuziphatha.
Neyroakantotsitoz
izigulane Neyroakantotsitozom andimvumeli kuphela hyperkinesis trochaic, kodwa acanthocytosis (utshintsho benza iiseli ezibomvu zegazi). phawu ukwahlula kule kwezimilo yi yoma (ubuthathaka izihlunu kweqondo eliphezulu nolusezantsi). Phakathi kwezinye iimpawu bahlule izifo: hyperkinesis ngomlomo ukuhlafuna iintshukumo, oku kuxhuzula iindevu lithe tso ulwimi kunye nezinye ubuso. Xa neyroakantotsitoze isigulane engathandi iskusyvaet ulwimi lwakhe, imilebe nezidlele kumphezulu engaphakathi igazi. Eyona nzima kule sifo kunye ne-dementia ezivelileyo ukugula.
Disease Lesch-Nai Han
izifo bekhubazekile e-nervous system aphazamisane umntu aphile ubomi ngokupheleleyo. Ezi ezimbi izifo ezinxulumene ne Lesch-Nai Han. Nobangela wesifo kukho intswelo ilifa hypoxanthine-guanine. Le chorea kubantwana lukhatshwa ukuphazamiseka kakhulu ekusebenzeni-luvo. Kwakhona ngezifo wavusa imveliso nangakumbi uric acid.
Ukususela kwinyanga yokuqala yobomi umntwana ubone ukulibaziseka kuphuhliso. Le nokoma ye imilenze kuboniswa ngenyanga yesithathu. Ukusukela kunyaka wesibini wobomi usana ukuba grimaces yobuso, ezo zihamba kunye iimpawu izitshanguba iphecana pyramidal kunye nophuhliso engqondweni libaziseko. Baby banokubenzakalisa emzimbeni ngokwabo Oluma umlomo wabo okanye iminwe.
chorea ebubonisayo
Chorea ebubonisayo kubantwana esizibonakalisa ibele okanye kwabaNtwana abasaKhulayo. Pathology ibhekisa izifo njengelifa. hyperkinesia ngokubanzi kule sifo tshwa kuphela xa usana lulele. Ukususela chorea Huntington kaThixo, olu hlobo leengxaki yahlukile non-progressors kunye nophuhliso eqhelekileyo ubukrelekrele. Ekwaluphaleni endala chorea ebubonisayo, Unako ukunciphisa hyperkinetic, ukuba ixesha qhagamshelana kwiziko lonyango.
iintlobo Secondary of chorea
Ezi ntlobo zixhaphakileyo zasesekondari sifo ingqalelo ezimbini: chorea kunye chorea ukukhulelwa.
Eyokuqala kuthiwa chorea Sydenham kaThixo. imbonakalo yakhe ukuze bandiqumbise usulelo streptococcal oyingozi okanye samathambo. ifomu onobulali luphawulwa grimace ngendlela ebaxiweyo, izimbo zomzimba ezichazayo, iintshukumo disinhibition. zaza zonke ngakumbi hyperkinesis trochaic wabonakaliswa yokuba isigulane kunzima ukuhamba, ukuthetha ngesiqhelo, ukuze aphefumle. Xa esi sifo ngokuthi "indihlaziya 'amadolo kunye nokusabela" siyanyangeka ", ukuphazamiseka ngokweemvakalelo ngokwenene, hypertension dystrophy.
chorea Pregnant - sisifo ibuyiswa ukususela ebuntwaneni. Oko kukuthi, kummandla umngcipheko le ngabo abafazi udibane umntwana ikwayala encinane. Pathology kunokwenzeka ngexesha lokukhulelwa yokuqala iinyanga 2-5. Ebudeni elandelayo 'umdla "imeko inokuba khona chorea. Unyango kwiimeko ezinjalo zinqabile, njengoko sifo liyalahleka ngokwayo emva kokuphazamiseka ukukhulelwa okanye emva zokubeleka.
chorea rheumatica
Livela kwesifo uza phakathi fever esikhathazayo samathambo okanye endocarditis, nto leyo sikhatshwa nesifo sentliziyo valvular. Kwiimeko ezininzi sifo ayikho enxulumene kule into, kwaye isifo kubonakala ngokuzimeleyo.
chorea rheumatism amaninzi kuchaphazela abantwana abaphakathi kweminyaka emi-6 no-15. Xa amantombazana, lo ngezifo kuxhaphake kakhulu. Inxaxheba kwinqanaba lokuqala esi sifo kuba kubangela inkxalabo, kuba iimpawu kufunwa grimaces, kwaye abazali a joke uyithabathe. Inkqubo iintshukumo ezincinane ngokuzenzekelayo le imilenze, kuqalwa iinzwane kwaye ukusasaza ngcembe wonke umzimba. Emva kweveki kufike ixesha umboniso, xa intshukumo lo mntwana ke ngok and kakuhle. Le meko ithintela usana ukuqhubeka imisebenzi eqhelekileyo, oko kukuthi, ukuba nidle, ukuba ahambe, ukubhala.
chorea rheumatism buyayigqwetha ubuso lomntwana amawaka grimaces. iintlobo kakhulu kwesi sifo ziyaphazamisana isigulane ukuba aphakame, ukuba imginye, ukuba athethe, yaye umzimba bahlale ezihambayo. Ukuba unesifo chorea, unyango kufuneka wenziwe ngocoselelo kwaye ngokungxamisekileyo.
ekuxilongweni
chorea eko kuvela ngenxa yokuziphatha engaqhelekanga. Xa uviwo lokuqala, ugqirha kufuneka ubambe ingxoxo kunye kumguli okanye usapho lwakhe. Ingakumbi kubalulekile ukwazi ukuba umntu ogulayo umntu kusapho esi sifo, elide njani iimpawu chorea, ukuba isigulane wathabatha iziyobisi, nokuba izigulo arhabaxa ubunzima. Ingcali Further kufuneka ihlole iintshukumo ngokuzenzekelayo. Kuyimfuneko ukuba afunyaniswe isifo kwaye afumane inkcazelo zizifo na ikhatshwe chorea, abangele ecaleni kakhulu ngokwasengqondweni. Iimpawu zezi zifo musa kusoloko kubonakala. Ngamanye amaxesha, ukuze ukungaphili ezinjalo kusekwangoko, imbaxa Surveys yenziwe. Uvavanyo igazi liya kubonisa inqanaba ngobhedu egazini kunye ubukho okanye ukungabikho kweempawu yokusabela arhabaxa. Ukongeza, yisa Itomography ikhompyutha magnetic livakale umfanekiso, electroencephalography.
unyango
Chorea - a ngezifo oko akuthethi ukuba isigulane ukuba aqhube ubomi yesiqhelo ngokupheleleyo, ngoko kufuneka ziphathwe ngendlela ngexesha nebanzi. Amaqhinga unyango kuxhomekeke izizathu ezibangela izifo. Ngokomzekelo, xa isigulane isifo Wilson ithe emiselweyo ukutya ezinomthamo ubuncinane wobhedu neziyobisi isenzo sakhe sibhekiswe ekunciphiseni ukufunxeka kwayo.
Chorea Huntington emiselweyo neuroleptics kunye okudambisa benzodiazepine. Ukuba chorea okubangelwa insufficiency ezingapheliyo yokumpompoza kwegazi yobuchopho, kukho imfuneko iziyobisi kuthoba uxinzelelo lwegazi. Vasculitis wathwala unyango hormone. Ukuba kuvela iimpawu ngokubanzi kakhulu, unyango kufuneka ezintsonkothileyo.
Ukunciphisa izinga iintshukumo ngokuzenzekelayo kunokwenzeka ngokusebenzisa zongenelelo ngotyando, xa kutshabalalisa ngumongo ventrolateral le thalamus. Chorea kufuneka uthathe iziyobisi ukuphucula ukusebenza ingqondo nesondlo, kwakunye iivithamini eqela B.
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