ZempiloDiseases and nemibandela

Syndrome Gilbert esithi: yintoni na? Oonobangela, iimpawu kunye nonyango lwe sifo

Isifo sikhatshwa kuphazamisa yibilirubin ukutya, oko echazwe kuqala ngo-1901 ngu A. uN Gilbert (Gilbert). Ngokutsho manani, kunye nesifo efanayo ijongene malunga 5-7% yabantu ehlabathini. Ngoko kutheni kukho Gilbert engqondweni, yintoni na yaye ziziphi iimpawu zayo? Ngaba kunokwenzeka ukuba kunyanga ngokupheleleyo esi sifo?

syndrome Gilbert esithi: yintoni na?

Ukuze uqonde ukuba yintoni kanye kanye esi sifo kubangelwa, kubalulekile ukufumana kuqala ezinye iinkalo yibilirubin ukutya. Le sombala yellow, nto leyo akhiwa ukubola mpilo esibindini (kombala sokuphefumla zegazi). It iguqulelwa kwifom ezamahala yellow mbala ndibotshiwe ancedisana kususwa kunye nezintso ezo. Ezo yibilirubin conjugated oluwe senyongo, uze emva koko ihamba kunye enyongweni kwisiqwenga wokudla kunye kwazona kunye ngendle. Xa esi sifo yibilirubin engadityaniswanga kwenye in ukunyuka egazini.

Gilbert engqondweni amaninzi olufunyanwa abahlali eAfrika, nangona kuqhelekile phakathi kwabantu bezinye iintlanga. Hi ndlela leyi, amadoda ubunzima kwesi sifo rhoqo malunga izihlandlo ezili-10 ngaphezulu kuneentombi.

Gilbert engqondweni; yintoni na yaye yintoni ebangela loo nto?

Esi sisifo ilifa apho linxulunyaniswa umsebenzi yemfuza ezithile. Ngenxa yoko, le hepatocytes isibindi runningaway glucuronyl ayonelanga. Yiyo le enzyme inoxanduva nomphetho owujikelezileyo yibilirubin ukuba glucuronic acid. Ngako oko, ukunqongophala ukwimo esebenzayo ikhokelela kumanqanaba aphezulu ezamahala mbala etyheli egazini.

Gilbert engqondweni: yintoni yaye ziziphi iimpawu zayo?

Uphawu iphambili yale sifo senyongo. Kufuneka kuqatshelwe ukuba ukwenyuka kwe esi sifo kuxhokonxwa yimiba eyahlukeneyo. Ngokukodwa, ukuvuthuluka imeko yabantu uyabonakala ngenxa luxinzelelo olungamandla, ngokomzimba, ukungondleki okanye indlala, ukusetyenziswa kwamayeza ezithile, ngokunjalo edlulileyo isifo engabalulekanga arhabaxa.

Ngokuphathelele songeniselo xi simahla yibilirubin egazini ibonakala yellowness ulusu kunye sclera. Ngophuhliso ezinye iimpawu zesi sifo zingenzeka. Ezinye izigulane ezikhala yintloko, ukuzikisa ongaboniyo, ukudideka, isiyezi, memory sokunciphisa. Maxa wambi kukho imvakalelo ixhala okanye uloyiko ukhathazeka phantsi wahlaselwa yokothuka, yaye ngamanye amaxesha badandatheke kunye ugwayi.

Ngokuqhelekileyo, kukho kwakhona ukuphazamiseka kwenkqubo yokwetyisa - na ukungabi namdla, isicaphucaphu, iintlungu esiswini, uphathwe kummandla lwesinye inyongo, isibindi yokuba iling'awukazi, nokuqunjelwa kunye norhudo. Kwezinye iimeko, ukukhula ukunyamezelana ukutya okuthile, ezifana carbohydrate.

Xa engekho uncedo kwangexesha ukuze sibonakalisa iimpawu ukusilela kwentliziyo okanye nokuphefumla, iingcangcazela, unxano ngokugqithiseleyo, ukuhlanza, iintlungu kwezihlunu, iindawo nkovu idumbile. Kwiimeko ezininzi kakhulu sisibindi luphuhla.

syndrome Gilbert esithi: Treatment

Ngelishwa ke, unyango lwezifo yemfuza asikho kunokwenzeka. Kwelinye icala, inkoliso sifo nabungozi - abantu abaninzi kangangamashumi eminyaka abakho ngesifo sakhe. yezonyango yokungenelela iyafuneka kuphela kwisithuba exacerbation. Ngoko ke, njengokokuqala iimpawu senyongo kufuneka udibane nogqirha. Bed ukuphumla, ukusela intabalala iziselo, iivithamini kunye ukutya efanelekileyo ukunceda bunjani ukutya. Kwezinye iimeko, isigulane emiselweyo phenobarbital, leyo kunciphisa inqanaba yibilirubin (ukusetyenziswa kweziyobisi ayikwazi lokungavinjwa, ekubeni idosi ezingachanekanga de iingxaki kunokwenzeka of ukusilela kwesibindi). Yokudla akufuneki kuquka iimveliso eziqulathe kwisigcinakaliso kunye notywala - ukutya kufuneka ibe nentlahla yaye ngokukhethekayo iyabiliswa.

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