Isifo Caroli esithi: Iimpawu and Treatment

isifo Caroli yeyona ukuphazamiseka entsonkothileyo kakhulu ukusebenza kwesibindi, isifo kwaye afumane unyango leyo ebangela ubunzima kakhulu oogqirha.

Yintoni isifo

Caroli Disease - onge isifo naso isibindi ebangelwe ukwandiswa bile duct, ibekwe ngaphakathi emzimbeni. Lubonakala kwi ukuba iimoto eqhelekileyo iphazamisekile duct ngxi kwenzeka nosuleleko layo ukulawula. Ngokufuthi sifo kuqhelekile ngabantu, kwaye iqala ebuntwaneni okanye lokufikisa. Inkqubela yenkqubo zophendlo lwezifo ixhomekeke kubungakanani neqondo umonakalo imibhobho ngaphakathi esibindini.

Isifo

Ukuza kuthi ga ngoku, kukho uhlobo elizimeleyo sifo Caroli ngayo amayeza engekhoyo. Noko ke, nangona oku, kukho iindlela ezahlukileyo ezimbini ze sifo. Ifomu yokuqala ungachazwa ukuba patency ezaphukileyo biliary, kunye nokusekwa elandelayo ngamatye.

Ifom yesibini ezinxulumene abanesigulo bekhubazekile hepatic. Kulo mzekelo, kukho ukwanda okuncinane kwezi yobisi kunye ukuyilwa amatye kunokwenzeka, nangona maxa wambi kwenzeka kwi zigaba ezithile zesi sifo.

bile duct Advanced ukuba uqhagamshele kwiindawo kwesibindi esinganyangekiyo yaye ngaloo ndlela libonwa ukwahlulwahlulwa eludongeni ukuqina kwi sayo cyst.

oonobangela

isifo Caroli libhekisela izifo iziphene ezivela ngenxa autosomal imo sofuzo zelifa. Ukuba une izalamane olusondeleleneyo ngezifo efanayo, emva kokuzalwa komntwana ngoko nangoko kufuneka ukuqhuba uviwo oluhlohliweyo, njengoko kukho amathuba omkhulu wosulelo lwe izifo njengelifa.

Kwezinye iimeko, esi sifo athelela yi nezinye izifo zophendlo lwezifo kwesibindi, nto leyo ebangela kubenzima kakhulu unyango.

The main Iimpawu

iimpawu zesifo Caroli kunokuba azibonakalisa a ngokupheleleyo nayiphi na ubudala abantwana kunye nabantu abatsha. Oku kungenzeka ukuba afeze iimpawu eziphambili sifo ezifana:

• walunywa;
• umkhuhlane;
• yellowness kancinane kwesikhumba;
• isibindi yesinye kwi Ngokucofa.

Ephawulwe ezibonisa kwezonyango sifo zidla ezinxulumene lubandakanywe nezenzo komtshiso oko. Ngokomthetho isifo Caroli banesifo kubantwana abangamakhwenkwe. Ndakuva exacerbation kuye esibukhali ukwanda kwinqanaba yibilirubin namhlophe cell wegazi.

isevisi ayikho

Ngaphandle kwento yokuba iimpawu zesi sifo ichazwe ngokwaneleyo, kodwa kwakhona uphawu nezinye izifo ezininzi esibindini. ukuxilongwa nokuba ukufumanisa isifo kunokwenzeka Caroli i-US nangexesha CT. Itomography ngekhompyutha njengenye yeendlela ezininzi efundisayo uviwo, kuba ungabona kakuhle ngokwaneleyo zonke ukunyhashwa imithetho. Ukongeza, cholangiography endoscopic kufuneka moshilongo.

umsebenzi Isibindi iimvavanyo ixesha elide ayitshintshi, kunjalo, kunye ukuqhubela phambili kwesifo kunye nenkqubo elide ukudumba kuhlalutyo zengqo- wegazi uyakwazi ukubona zonke iimpawu cholestasis.

Ngenxa yokuba izigulane basemngciphekweni cholangiocarcinoma, kongezelelwa kufuneka wenziwe kunye nokuhlolwa lokukhangela ubukho kwabamakishi ithumba.

Iimpawu zonyango

Phambi sifo Caroli izikhokelo zonyango kufuneka babonwe sithe, ngenxa yokuba lo leengxaki luphucukile ngokwendalo. Treatment kuthetha ngokusetyenziswa antibiotics ebanzi-spectrum, kwaye ursodeoxycholic ubume nolawulo acid ukuthintela calculus ukwakhiwa.

Ukongeza, unyango iquka:

• analgesics;
• amatye litholysis;
• yamanzi biliary.

Phezu umbusi, cholangitis, okanye ezinye iingxaki unyango ubovu akukho kwahluka nokunyangwa cholangitis yebhaktiriya. Kubalulekile ukususa ubomvu uze zokuhlanjululwa lwenziwa we bile duct wenziwamkhulu, ndayinikela antibiotics ukunceda ukususa usulelo.

Olu tyando lwenziwa kuphela kwimeko exacerbations rhoqo okanye ukusetyenziswa ngempumelelo iindlela angqingqwa. Umthamo ngoncedo ngotyando zinokwahluka kakhulu. amatye kuphela okanye izicatshulwa biliary asuswe.

Kwimeko izicatshulwa ukwanda ngamandla kakhulu kwaye biliary inyongo yokunqaphela, ugqirha uyakwazi ukuqhuba kususwe omnye nomhlehlo wesibindi. Kwiingozi ezimasikizi, insufficiency hepatic phambi okanye iimpawu angakwazi kwi ithumba, esinye isibindi ukuze kukhuthazwa kwisizalwane esisondeleyo.

Ukuze ufumane iziphumo ezintle, oogqirha abaninzi Sicebisa bachitha ezithile isibindi abohlukeneyo nkqu ukungabikho kweempawu kakhulu kwi sikwinqanaba lokuqala sifo. Noko ke, kukho usulelo yinto contraindication ku abohlukeneyo. izigulane elingama emva abohlukeneyo abanesigulo bekhubazekile aye Ukongezelela kwafunyaniswa cholangitis ngexesha abohlukeneyo, kuba kunokuba phantsi.

Abantu abane kwesi sifo kakhulu ntle, ekubeni likakade kunokwenzeka iminyaka emininzi. Noko ke, kunqabile kakhulu oko kukhokelela ekufeni malunga nesigulane eso.

isifo Caroli

Disease Caroli kaninzi ezinxulumene abanesigulo bekhubazekile hepatic, okutsho ukuba isifo Caroli. Zombini ezi ezimbi akhiwa ukuphazamiseka ifomu biliary phantse twatse xa esibindini umcu kwinqanaba lophuhliso osandul. Lesi sifo esasulela kwisizalwane esisondeleyo kwaye intlungu babonakaliswa esiswini kunye opha varices esophageal. Neonates inokuba indibanisela iimpawu eziphambili abanesigulo hepatic awazalwa enaso, isifo Caroli kunye nesifo sezintso polycystic.

Esi sifo ibhekisa naso inyongo obucala cyst, ke, loo nto yinto enqabileyo kakhulu ngabantu abangaphantsi kweminyaka engama-30. Kwiminyaka embalwa yokuqala ngezifo kwenzeka phantse nazimpawu, yonke imihla ukwandiswa bile duct musani ukubacaphukisa yokunqaphela ngayo ibile ducts, nto leyo eya kudala iimeko ukuze kwakhiwe amatye kunye nosuleleko ukulawula. Xa zisetyenziswa kunye nezinye iimpawu ebona senyongo, libonisa phambi cholangitis.

It sabhiyozela umonakalo kwesibindi ikakhulu ekhohlo-kabini, kodwa kwakhona kuba sineendlela ezimbini kwezinye iimeko.

Kwezinye iimeko, isibindi namandla kangangokuba kunokuchaphazela namanye amalungu. Ngoko omnye iingxaki nga ozakuthathwa kukuvela ukusilela kwezintso.