Zempilo, Diseases and nemibandela
Igazi aplastic
igazi Aplastic imbaxa sisifo igazi. Inxulunyaniswa nokuphungulwa imveliso granulocytes, neeplatelets kunye neeseli ezibomvu zegazi wamathambo. isigama Medical libhekisa kwisigulo edakumbisayo eli hematopoiesis sifo.
igazi Aplastic luphawulwa ukuncipha inesipani iiseli ezibomvu ubomi, sikhatshwe ukutshatyalaliswa igazi iseli ezibomvu iiseli lomongo wethambo ngexesha zonke izigaba zophuhliso.
Esi sifo iba nefuthe elibi kakhulu umsebenzi wamalungu ezininzi. Ngoko ke, amanyathelo diagnostic ngexesha kunye nonyango bolu kwesifo ngcono kakhulu umgangatho wobomi.
igazi Aplastic uyakwazi ukuphuhlisa nanini na ubudala. Kodwa ke kaninzi, ngenxa manani, ezisengozini sifo ezindala ngaphezu kweminyaka engamashumi amahlanu.
Unobangela sifo kuhlala ayaziwa apha malunga nama-80% amatyala.
Kungenjalo, ngokutsho iingcali zophando, wavele, isifo okubangelwa zizinto zangaphandle, ezifana nokusetyenziswa elide iziyobisi (antibiotics, iziyobisi antituberculosis, sulfonamides, kunye namanye amayeza antiinflammatory).
igazi Aplastic ngebala kunye inhalation elide umphunga mercury, oyile, iikhompawundi benzene, kwakunye ngenxa yokuba sesichengeni kwemitha.
Amanye amatyala karhulumente malunga nophuhliso iinkqubo ezosulelayo emzimbeni, zezigulo ezahlukeneyo ekusebenzeni iinkqubo omzimba yonyango.
Izizathu ngasentla iingcali bathi kwifom abazifumene kwesi sifo.
Uhlobo ilifa isifo kuboniswa iintlobo ezininzi.
Isifo ingahluka bubukho okanye ukungabikho ukungaqheleki iziphene kuphuhliso kunye ukoyiswa lilonke ukuyilwa iiseli ezibomvu zegazi. Kwakhona, kukho anaemia kunye ngezifo uyakhetha.
Iimpawu ixhomekeka kuhlobo imeko.
Iimpawu ze Fanconi anemia kuvandlakanywa yabantwana yasekuqaleni. mgaqweni bekhubazekile ichazwa iziphene kakhulu kuphuhliso esiqwini amathambo (clubhand, inani engaphelelanga leminwe esandleni, njalo njalo). Ngelo xesha kukho jikelele ubuthathaka, intloko ebuhlungu, susceptibility ukuba umkhuhlane. Uvavanyo igazi ityhila high ESR. Ngokuqhelekileyo, eli urhulumente kuqhubeka de kweminyaka elishumi elinesibhozo kwaye ibulale ngenxa usulelo ngengozi okanye ukopha.
Xa igazi Oestrich-Dameshek akukho bekhubazekile ukungaqheleki. Olu hlobo sifo kunqabile waphawula.
Xa igazi, Diamond Black fan kwiimeko ezinqabileyo, kukho umonakalo amehlo elimele. iimpawu Common yale meko ulusu umbala nombala kunye udakada banzi. Uvavanyo igazi utyhila haemoglobin kwanciphisa kunye nokwanda okukhulu lomlinganiselo erythrocytes kunye leukocytes. Njengoko yokusebenza ibonisa, uninzi lwezigulane musa Zinokuphila zide zibe neminyaka engamashumi amabini.
ikhondo Acquired isifo etsolo kwahlukile emathunjini intabalala, zezintso, ukuthetha kwam ngeempumlo nesikhumba ukopha. Ngelo xesha ukuphuhlisa nomkhuhlane.
Kuba iintsuku eziliqela, izigulane babone ukuhla kakhulu ukubala zegazi, iiseli ezimhlophe zegazi kunye neeseli ezibomvu zegazi. Survey ityhila inhibition of weseli nokwanda kunye nokuthotywa egazini. Ukufa kwenzeka kwiiveki ezine ukuya kwezisibhozo.
ifomu Subacute luphawulwa ukopha ngaphantsi kakhulu. Ubomi ukususela ekuqaleni kwesi sifo ziyahluka ukusuka kwiinyanga ezintathu ukuya alishumi elinesithathu.
Ifom okondeleyo sifo flow kade. Lubonakala yi Uxolelo ixesha elide.
Xa izigulane insufficiency ezisebenzayo adrenal kwenzeka anemia normocytic normochromic in ngobulali. Le meko kukuba kwiimeko ezininzi kunzima ukuchonga eyaneleyo, ngenxa nokuncipha ngaxeshanye umthamo plasma.
Ngenxa sasiphikisana umsebenzi lwesiqu hepatic iphuhlise anemia macrocytic.
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