ZempiloDiseases and nemibandela

Mastocytosis kubantwana: oonobangela, unyango kunye neziphumo

Abantwana abagulayo, yaye lo mntu ukuba ahambe. Kaloku, ukuba isigulo phe yakhawuleza, kodwa kuyenzeka ukuba yena umntwana iminyaka emininzi, okanye nangakumbi - yobomi. Hayi, abo bazali abaziyo indlela yhuu impumlo ebandayo kunye esihambisayo. Kweli nqaku siza kuba sathetha ngezi iinkathazo, siya sithethe ngale nto sifo njengoko mastocytosis ebantwaneni.

Ngokufutshane malunga nokugula

Esi sifo, xa uqala kuqala, oko kubangela inkxalabo. Kodwa ke kuyimfuneko ukuba angakhululeki unyango, umntwana emzimbeni kuqala ukuqokelela iiseli namanqatha. Ekuhambeni kwexesha, isifo akuyongozi ungakwazi ukuguqula kwifomu wolusu.

Mastocytosis Kunqabile, kaninzi abantwana ubunzima kulo. Oku kuchaphazela kuphela eluswini, kodwa amanye amalungu. Malunga namashumi alithoba ekhulwini abantwana nesi sifo bayahlupheka ukusuka urticaria pigmentosa. Ngelo isanda xa kwafunyaniswa ukuba mastocytosis ebantwaneni, unyango kukusetyenziswa antihistamines. Ngeli xesha, ngokuyimfuneko esweni ekuhambeni sifo ngxabano.

Amashumi asixhenxe anesihlanu ekhulwini amatyala, esi sifo kwenzeka abantwana abangaphantsi kweminyaka emithathu ubudala kwaye komntu akuxhomekekanga ekuzithandeleni besini umntwana. Le umyalezo kunye Pathogenesis ayikenziwa kakuhle ngokupheleleyo, kwaye ngokuchanileyo kubizwa ngokuba unobangela sifo akunakwenzeka. Kukho uluvo lokuba ngamanye amaxesha sifo sisasazwa ngendlela lubalaseleyo autosomal.

iintlobo zezifo

Ngokusekelwe ngeempawu zesi sifo, mastocytosis abantwana kunye nabantu abadala liye ifomu elilandelayo.

  • Esikhumbeni, ebuntwaneni. Waphawula ngabantwana ukuya kwiminyaka emithathu. Ekubulaleni izibilini zilahlekile. irhashalala unyamalale ngokupheleleyo ukufikisa yaye akayi kuvela. mpawu ngamanye amazwi ngamandla kufuneka lungisa, kwaye okona kubaluleke kakhulu, unyango ngexesha.
  • Cutaneous abafikisayo mastocytosis kunye nabantu abadala. Kukho visceral, kodwa hayi inkqubela kwi ifomu elinikiweyo.
  • System. Amaninzi, olu hlobo sifo awayezibona abadala. Kukho utshintsho eluswini, luqhubela phambili umonakalo ilungu lwangaphakathi.
  • uhlobo olubulalayo (lwemasti iseli leukemia). Olu hlobo esi sifo siphantse sibe nokubulala. iiseli imasti zitshintshiwe. Bona kuchaphazela izibilini nezihlunu, ingakumbi ithambo kunye negazi neuropathy. Kufuneka Makukhunjulwe ukuba ulusu obubonakala badla ngokungabikho ngokupheleleyo.

Types of kolusu

Kukho iindidi ezintlanu kolusu kwi sifo.

  • mastocytosis Maculopapular ebantwaneni. Photo ubonisa indlela umntwana ukhangela kweli xesha. baby ulusu sigqunywa ngokupheleleyo namabala amancinane kunye papules kubomvu-mdaka.
  • uhlobo ezininzi lenzeka. On the isikhumba eninzi amaqhina ashinyeneyo. Iiplastiki omthubi, ezipinki, ebomvu. ububanzi sabo malunga ngesentimitha enye, uhlobo - hemispherical.
  • Mastocytoma (wodwa node). Kubonakala node. ububanzi baso ngeesentimitha ezimbini ukuya kwezintlanu. Inokuba uhlobo kakuhle okanye ukushwabana. mastocytosis bodwa abantwana kaninzi kwenzeka umntla, iingalo kunye nentamo. Eyona basengozini kakhulu kolu hlobo iintsana sifo.
  • Ehlasela. Eqalisa ukuba ukuphazamisa abantwana besebancinane. Le kolusu ke zakha umbala otyheli-mdaka. Amaninzi, ukuba ibekwe kwamakhwapha, phakathi ezimpundu. Babonakale neentanda.
  • uhlobo Teleangiektatichesky. Xa abantwana inqabile.

Zokugula

Njengoko kukhankanyiwe ngasentla, impendulo enokukucaphukisa enjalo isifo esiyingozi ukuba kunzima kakhulu, njengoko umyalezo wayo ayaziwa. Kodwa kuyenzeka noko ukuchonga unobangela mastocytosis ebantwaneni. Komorowski wabahlula ngokwamaqela ezisekelwe ubudala bomntwana.

  • Kubelekwa. Unobangela sifo ngokuba allergen ukutya. Ugqirha kufuneka iqatshelwe apho usapho ngaphambili ubunzima kwesi sifo.
  • Zingane (iminyaka emithathu). Kunegalelo ekuqaleni zoqhagamshelwano kunye nokusingqongileyo.
  • Abakwisikolo sabantwana. Kuzo zonke izizathu ngasentla, kongezwa zokudlala uyaliwa.
  • abantwana School sigula ngenxa yoxinezeleko, nezengqondo, ntshikilelo.
  • Abantwana badla ubunzima emva ukubila. Ukuze esinye sezizathu zibandakanya ukuqeqeshwa lweembaleki.

Ukuze imiba jikelele ezibangela isifo, kufuneka ibandakanye inkqubo buthathaka omzimba. Yaye uza kuba umdla ukwazi ukuba kwintsapho enye ubunzima kwakwizizukulwana eziliqela, kokuba kuchazwe ukuba esi sifo unalo uhlobo njengelifa.

zesifo sifo

Mastocytosis kubantwana, njengazo zonke izifo uneempawu zaso. Makhe sithethe ngazo, nangona ngaphambili kwicandelo "Types of kolusu," sele kuqhutywa ngeempawu zesi sifo. Kodwa njengoko bathi, loo nto ayithethi buhlungu ukuba ukukhumbula.

Ngaphezu kokuba umntwana lokugula olitshijolo, akazange afune ukuba ukudlala lonke ixesha ukulungele ukuba abazali ezandleni ngaphezu kwakhe;

  • kukho ukurhawuzelela olunamandla;
  • umzimba ugcwele amabala sayingqombela-pink;
  • ububomvu zitshintshele ibe amaqamza kunye ulwelo ngaphaya okanye igazi;
  • yabangxamayo kwanwenwa buti, ubuso, izandla (xa kungekho unyango uncedo);
  • baby isikhumba izokhula kwaye bathathe Tint elityheli.

Imida zivelile ezakhiwe ichazwa ngokucacileyo, umphezulu akuthethi uxobule. Kwiintsuku ezimbalwa emva kokuvela amabala abomvu ijike ibe limnyama.

Ngamanye amaxesha acne ngokwalo bayeke ukukhula, kodwa kukho amaxesha apho bonke isikhumba abachaphazelekayo kwaye iqala lilide yabo izibilini.

imilo wodwa

mastocytoma sodwa - yinto ithumba olunye wabumba kwiiseli imasti. Olu hlobo kakhulu inqabile, kodwa kufuneka uyazi ngayo. Ngaba mastocytosis bodwa abantwana (zibonwa kwifoto) ithumba Ukwakheka. Le ukwakweli emzimbeni, ngokufuthi ngasemva, esifubeni, intamo kunene. Ukwesaba kwangaphambili akukho mfuneko. kwedatha yeenkcukacha-manani zibonisa ukuba ngo-90% yamatyala le ndawo usombulula kunye nexesha. Ngu lokufikisa komntwana kungaba enzonzobileni ngokupheleleyo. Ngokuba lo hlobo sifo zimpawu ukurhawuzelela eqatha ukugxojwa izibilini.

Ngamanye amaxesha uhlobo wodwa of mastocytosis ingathatha ngenxa nevi ulwehlo. Ukukhokela kugqirha sokususwa yemfundo umntwana. Ayizi kuzisa iinzuzo daze yaye abazange ukusombulula le ngxaki.

Ukuba itakane rascheshet inxeba okanye yenzakalise, endaweni yayo kukho maqampu.

ekuxilongweni

Ngubani na qhagamshelana ukumisela mastocytosis ebantwaneni, kubangelwa? Le miba umdla abazali abaninzi. Kuyo nayiphi na imeko, balibala ukutyelela ingcali ayikho imfuneko. Okufunekayo kwimeko silubone amatshatshazi eluswini idilesi komntwana ukuya kugqirha-wesikhumba. Uya lokuxilonga, ukuba kuyimfuneko, thumela kwamanye nabo. Xa kungekho tyala musa ukuqala unyango lwabo. Ngapha koko, akuyazi ukuba yintoni iimeko negalelo inkangeleko yabangxamayo.

Ugqirha uya kuvanya usana lwakho ngokusondeleyo. Ukuze ezi njongo, oko iqhele ukusetyenziswa Dermatoscope. Nale izixhobo akubikho iimpazamo kokuxilongwa. Emva koko, imibuzo malunga mntwana uya kunikwa abazali. Impendulo kufuneka ngokufanelekileyo, uyacebiswa ukuba ukukhumbula zonke izikhalazo ephuma emlonyeni wembewu. Ukongeza, iimvavanyo yelebhu iya kwenziwa. Siza kufuneka athathe uvavanyo lwegazi Kwathi uxilongo ultrasound amalungu zangaphakathi ukuze uphephe uhlobo lwenkqubo yemfundo sifo.

unyango

Mastocytosis bene ebantwaneni. izinto zayo, kangangoko kunokwenzeka, bazimisele. Lifikile ixesha lokuba uqale unyango. iinkqubo ezithile abangekenzi wadala. Ukuphucula imeko umntwana kusetyenziswa unyango nomqondiso. Injongo unyango - ukunciphisa umsebenzi wophuhliso cell imasti. abantwana abadala kunye nabantwana emiselweyo:

  • Iziyobisi nxamnye komzimba: "Suprastin", "Tavegil" kunye nabanye.
  • Iziyobisi ekwaziyo uzinzo ukusebenza iiseli ngolunya.
  • PUVA therapy. isikhumba liphathwa ukukhanya eyingozi. Kuya kuthatha iiseshoni ezingamashumi amabini anesihlanu. Oku kusetyenziswa xa kuthe antihistamines musa ukuveza iziphumo. Le nkqubo iza kunceda ekunciphiseni inani amatshatshazi eluswini.
  • arhente Cytotoxic (uhlobo lwenkqubo yemfundo sifo). Isifo nabo ukuba ukunyanga, kodwa isantya kwaye ukunqanda ukukhula amafutha kangangoko kunokwenzeka.

Fumanisa unobangela mastocytosis ebantwaneni, unyango kwezinye iimeko, inokwenziwa kusetyenziswa iiresiphi amayeza emveli.

iindlela Treatment abantu

Kwangoko alumkise, bahlukane esi sifo ngale ndlela kunokwenzeka kuphela emva kothetha-thethwano kunye nogqirha wakho. Izityalo kunceda ekunciphiseni ngobunzulu sokudlathuka kweenwele kunye kwinwebu isikhumba. A zokupheka ezimbalwa:

  • Yekoriyandire (imifuno umgubo) oluxutywe iswekile olungumgubo ngokwesahlulo kwelinye ukuya kwelinye. Sebenzisa wesiqingatha itispuni phambi izidlo.
  • Nokufakwa ivy. Anetispuni oki ixolo kunye ivy amagqabi ugalele amanzi (ilitha enye) ukubilisa, kwaye banyanzelise ukuba aphole. Lenza a cutha. Le ndawo obala ibamba imizuzu engamashumi amabini.
  • Nokuhlanganiswa umba. Thatha enye icephe umba eyomileyo. Wagalela iglasi yamanzi abilayo. iindawo asha mayicocwe esi sisombululo izihlandlo eziliqela ngemini.
  • Mastocytosis kubantwana ithathwa iibhate ngaphezulu esintu. Xa ageza vodichku wongezelela: chamomile, celandine, umba, nomfundisi series.

Ukusebenzisa ezi ndlela lokuphelisa ngokupheleleyo umntwana akakwazi le ngxaki, kodwa imeko yakhe lula.

Iziphumo sifo

amaxesha amaninzi kulo lonke eli nqaku ngokuphindaphindiweyo: ukuphawula kwamaqhakuvana kwi umzimba usana, ngoko nangoko qhagamshelana nogqirha wakho. Emva ngokupheleleyo isifo akuyongozi nga phambili ingxaki ezimandundu: umonakalo omzimba kunye nokufa.

Abantu abane kwesi sifo kuxhomekeke unobangela mastocytosis ebantwaneni. Le ifoto ibonisa ukuba iingxaki zisoloko ngokwazo kwaye umzimba komntwana ayikho amatshatshazi.

Esi sigqibo ayikwazi makenzelwe sisilonda esidumbileyoesingaphakathi systemic. Ukuba leukemia iseli lwemasti banesifo, akukho mfuneko ukuthetha malunga nophuhliso intle. Yiyo loo nto ke ukuphinda kwakhona: musa angakhululeki unyango. Ngoko nangoko qhagamshelana nogqirha wakho.

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