Hemolytic-uremic syndrome - ntoni na?

Hemolytic uremic syndrome yi uphawu, nto leyo ebonakaliswa ngokohlobo igazi hemolytic, OPN kunye thrombocytopenia. Kuba okokuqala esi sifo kuchazwa ngo-1955. Ngokutsho kweengcali, malunga nama-70% amatyala uxilongo xa abantwana kunyaka wabo wokuqala bezelwe, kunye iziganeko ezimbalwa kuphela kubhalwe abadala. Kweli nqaku siza kuthetha ngesi sifo, kwaye bajonge ukuba baphathwe ngayo iindlela zale mihla hemolytic uremic syndrome.

izizathu ezibonakala

Uphuhliso kwesi iingcali sifo kwi namhlanje lu dityanisiwe izinto ezininzi. Ubukhulu becala lo lohlobo ezinobungozi ngqo umonakalo capillary endothelium ukuze ngokuba glomeruli. Kwelinye isizathu isandla ilala DIC kunye umonakalo ukuba erythrocytes. Kukholelwa ukuba akwazi nokuba yonakele ngexesha sicatshulwa ngokusebenzisa emithanjeni ka glomeruli ngokwabo, leyo ke yona ezele amahlwili fibrin.

iimpawu eziphambili

Hemolytic-uremic syndrome kwenzeka ikakhulu abantwana kunye ukwehla ngokukhawuleza imveliso umchamo, kodwa kungekho iimpawu ezicacileyo emzimbeni kwaye kwisiqalo yemida VEO gqitha eqhelekileyo. Ukuba umntwana uzelwe nefiva okanye ukugabha wabonakala kakhulu ukuba isifo siqhubela phambili ngokukhawuleza - kwakukho nokudumba lobuchopho. Amaxesha amaninzi, hemolytic uremic syndrome kuhamba umntwana sakuba ngebala, kwiimeko ezinqabileyo, kunye kuqhume ezincinane.

ekuxilongweni

Ukuba uyayazi imbangela efana hemolytic-uremic syndrome, Uze udlulele uthotho lweemvavanyo, kuquka uhlalutyo igazi epheleleyo. Kuphela emva kokuba uviwo epheleleyo isigulane ukuthetha unyango olungaphezulu.

iindlela Modern zonyango

ukufa uphethwe Kutshanje awunikwe eliphezulu kakhulu (80 ukuya kwi-100%). Noko ke, oosonzululwazi isoloko ikhangela isisombululo kule ngxaki. Ngaloo ndlela ke udale izixhobo ngokuba "kidney ngumntu", Bulelani apho meko itshintshe ngokupheleleyo. Namhlanje, ukufa phantse ziphinde zenzeke (phakathi amabini aneshumi pesenti). Ukuze kube nje ngexesha Ubhaqo isifo kade, ngokunjalo kuphuhliso kweenkqubo ayibuyiseki umva ebuchotsheni ngenxa ukudumba yayo. Kufuneka kuqatshelwe ukuba loo uphethwe Nedlac uremic hemolytic syndrome, ngokubanzi ifuna ukusuka kwiiseshoni ezi-2 ukuya ku-9 (yonke imihla) usebenzisa i "kidney yokufakelwa". Ngesi dialysis iingcali uyakwazi ukugcina amanqanaba okuqhelekileyo metabolites, kwakunye ukuthintela ukudumba ebuchotsheni.

Outlook

iindlela Modern ukuvumela abantwana ukuba ukuhlangabezana nale ngxaki. Noko ke, oku kunokwenzeka kuphela xa kuthe nokuba isigulo ibhaqwe buyatshintsha zokuqala. Kungenjalo, ukuba nokwenzeka ngokupheleleyo kuphila asezantsi noko. Ngokutsho kweengcali, imeko kungekho impendulo entle ilungu lomzimba emva kwiiseshoni 2-3 wehemodialysis, iingqikelelo ezimbi kakhulu.