Zempilo, Diseases and nemibandela
Ezidalwa yebhinqa. Yintoni na?
Ezidalwa okanye ngokwenzululwazi, yebhinqa dwarfism, kukho leengxaki apho kukho ukulibaziseka yokukhula ngokomzimba kunye nophuhliso, oko kubangelwa kuyondelelaniswe nokuqhwalela kunye secretion hormone okukhula (eyaziwa ngokuba hormone nokukhula).
Le ngezifo kunqabile kakhulu, abantu abamalunga nama-2 kwama-10,000 dwarfism yebhinqa ibanjiwe kubini kuxhaphaka kakhulu amakhwenkwe kunokuba namantombazana. Ukwanda kwabantu ingqalelo nenomlanga ukuba ungaphantsi kwama-130 cm kunye nabafazi efanayo - ngaphantsi kwe 120cm.
Izizathu zixhaphakileyo zezi zilandelayo:
• kwasekuzalweni (in Esibelekweni cipande yebhinqa abunjwe ngokungachanekanga)
• limala (ezi ziquka zombini generic)
• yebhinqa Ithumba okanye izakhiwo ezingqongileyo,
• yofuzo,
• negcushuwa, isifo sephepha, sarcoidosis,
• kugqithiselwa ichemotherapy okanye unyango radiation.
Noko ke, ngaphezu kwesiqingatha oonobangela dwarfism kunye ahlale abangaziwayo.
Njengoko ezidalwa yebhinqa okhula?
Ubunzima kunye nobude kwabantwana kunye secretion zaneleyo hormone okukhula ekuzalweni zange sahlukile kumaxabiso ahambelanayo abantwana esempilweni. iimpawu zokuqala kakhulu akholisa ukubakho abantwana de kweminyaka engama-2-3: aba bantwana musa uqala ukugcina up kunye nokukhula eqhelekileyo noontanga babo. Kabukhali ukwehlisa izinga lokukhula, apho ayidluli 3.4 cm / ngonyaka (ngesantya nama-8 cm / yr). Nangona ukulibaziseka ukukhula, olinganise echanekileyo umzimba umntwana ayagcinwa.
Ukongeza, insufficiency yebhinqa njengoko eyaboniswa mpawu zilandelayo:
• lokungaphuhliswa uhlelo zokuzala,
• waphawula inkqubo luyalambatha dystrophy,
• hypotension,
• Ukunciphisa isantya Ukuqina kwe amathambo, uphuhliso amazinyo ezaphukileyo notshintsho,
• ukuba kukho ithumba kwi ingqondo yebhinqa okanye kwiindawo ezingqonge le ebuchotsheni, ukongeza kwezi mpawu, uqala umbono ngakumbi imfiliba.
Ngokuqhelekileyo, uphuhliso engqondweni kule sifo musa ubunzima, ngokuqhelekileyo izigulane kufuneka memory elungileyo.
Ukuze uqinisekise lokufunyaniswa "yebhinqa dwarfism" kuyimfuneko:
• avavanyelwe hormone yokukhula. Ukongeza, kuya kufuneka uvavanyo ukuchonga ezinye iihomoni. Mhlawumbi kufuneka iimvavanyo hormone: kuqala kumiselwa inqanaba yesingqiniso hormone egazini, emva koko ethatha umguli ichiza esichaphazela ummiselo incindi yedlala, emva kwexesha elithile, uhlalutyo iphindiwe.
• ummandla Run X-ray sella kunye ukakayi ukujonga ubungakanani ingqondo yebhinqa. Kwakhona ukucacisa kubanjwe kwikhompyutha okanye livakale magnetic ufaniso yobuchopho, ukuba inkqubo yalula, bavumela ukuba ubone indawo iinkcukacha kummandla yebhinqa kunye engqongileyo isicwili sobuchopho. Ukuba kukho ukonakala umbono, kuyimfuneko ukuba adibane zamehlo.
ezidalwa pituitary ngokuhlukunyezwa endocrinologists. Indlela esisiseko yokubuyisela amanqanaba hormone ukukhula emzimbeni unyango replacement: ukusetyenziswa kwezindlela esisigxina hormone ukukhula. Ukuququzelela ekubaleni idosi kunye nokulawulwa hormone ngoku ilungiselelwe usiba ekhethekileyo ngenaliti.
Ukuba unyango eyaneleyo ukunyuka izinga lokukhula kumanqanaba yesiqhelo (8-12 cm / nonyaka), phambi kokuba unyango, njengoko umthetho, kukho cm 3-4 kuphela / ngonyaka. Xa ufikisa kufuneka zifakwe kwi-hormone sex irejimeni yonyango.
Nokulunga unyango kuxhomekeke ngqo kwi ngoonobangela sifo, iye yabangela. Kakhulu, izigulane unyango eyaneleyo ukufikelela ukukhula eqhelekileyo kwimo engqongileyo.
Jonga iingcali kwimiqondiso yokuqala yebhinqa insufficiency!
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