ZempiloDiseases and nemibandela

Ehlers Danlos Syndrome,

Ehlers-Danlos syndrome - ezivame kakhulu njengelifa
isifo kwizicwili. Le izehlo Lena enye
ikhulu lamawaka kubelekwa. Phantsi eli qela syndrome edityanisiweyo
izifo ezo zisekelwe collagen isiphako esisiseko
kwizicwili. Ilungiselelwe Iintlobo ngaphezu kweshumi izifo, ezahlukeneyo kwezinye iinkalo. iimpawu zangaphandle eziye Ehlers-Danlos syndrome, ochazwa ukwanda extensibility, isikhumba sengozini, ukushukumisa amalungu kunye iimpawu ukopha diathesis. Kukho kwakhona ngokoyiswa inkqubo yokuphefumla kunye nemithambo yegazi, inkqubo musculoskeletal, isiqephu zesisu.

Isikhumba izigulane unesifo Ehlers Danlos syndrome, ethe, zingcakacile, kakuhle zigxunyekwe emzimbeni wengxaki. Ngelo ukonzakala nakancinane nokopha yesikhumba hardhealed kwenzeka, kwindawo apho loloyiko wakhiwa umphezulu ukushwabana. Syndrome Ehlers -Danlosa luphawulwa ukushukumiseka okungaqhelekanga namalungu, leyo zibangelwa dislocations ezingapheliyo kunye subluxations namalungu. Kwiimeko ezininzi sifo ihamba diathesis ukopha, xa izigulane bazigruzule lula kwaye hematoma kuvela eyendawo ezahlukeneyo. ukopha lohlobo evela iphecana zesisu, iintsini, isibeleko.

Kuba ezinye iintlobo zezifo luphawulwa ibutho semehlo neenyembezi
amehlo. Ehlers syndrome - Danlos syndrome maxa wambi kuhambisana engalunganga
ukuyilwa kwamazinyo kunye nokungabikho buso, ukuphuhliswa periodontitis.
Ukunyhashwa inkqubo musculoskeletal zibonakale ngohlobo deformation ye esifubeni
iiseli kunye ugobile spinal. Izigulane amaninzi zifumaneka Ithemba
kwasendaweni ezahlukeneyo. Emva kokoyiswa izibilini ngenxa intliziyo
neempahla, inkqubo bronchopulmonary, aneurysms nemithambo kwakheka ezininzi
ingqondo kunye aorta. Emva kokoyiswa intliziyo akhiwa imikhuba ezahlukeneyo.

Ehlers-Danlos Syndrome Treatment

Izifundo ezahlukeneyo kwenzelwa uxilongo oluchanileyo sifo
izakhiwo ezizodwa inpatient. Zisa ubunzima obukhulu
iingxaki yokubelekisa and ngotyando kunye nezigulane abaye kwafunyaniswa kunye syndrome
Ehlers-Danlos syndrome. Unyango sibhekiswe ngokuyintloko uzinzo kunye
bunjani iinkqubo pathways kwinkqubo luvo kunye nemithambo yegazi,
inkqubo weentshukumo. Therapy esi sifo ibandakanya
wamkelekile uluhlu olubanzi B iivithamini, A no E. iziphumo Good ukunika
carboxylase kunye ascorbic acid, iinaliti hormone okukhula (somatotropin
hormone) carnitine chloride. Izigulane Kucetyiswa amayeza ukuphucula umsebenzi ubuchopho (Pantogamum, Nootropilum, Riboxinum, rutin, Pananginum). Ngaphandle kuyimfuneko ukuba naloo zonyango physiotherapy rhoqo njengoko laser lokugqojozwa, unyango ngemagnethi. Izigulane kwakhona ukumisela izifundo ze physiotherapy kunye yokuthanjiswa, iiseshoni Reflexology.

Xa unyango lwezifo ingqalelo enkulu kufuneka inikwe nakujoliso olutsha ezigulo ezondeleyo
usulelo akhiwe emlonyeni nasopharynx (adenoids, ezondeleyo
tonsils, sinusitis, amazinyo carious). unyango olulodwa onaso de
Ithe yaphuhliswa. Kunconywa ukuthotyelwa indlela nokuthantamisa yobomi nendlela
izithintelo esinokubakho imithwalo emzimbeni. unyango lingaze lubandakanya utyando ulungiso sengozini thoracic, ukususwa pseudotumour, unyango ezimbi iliso, intliziyo, njl Iingqikelelo ubomi kuxhomekeka kakhulu kuhlobo syndrome. Uthintelo genetic counselling.

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