ZempiloDiseases and nemibandela

Myasthenia Gravis: iimpawu, isifo, unyango

Namhlanje, zininzi izifo sokuhlasela. Umntu ukubabulala encediswa unyango zikhethwe kakuhle, ngoxa abanye besamkela kunyango, kanye into kuphela ekwaziyo amayeza - ukuthintela exacerbations.

Eli nqaku liza kuthetha izifo ezifana myasthenia gravis: iimpawu, isifo kwaye afumane unyango lwesifo - zonke ezi zihlandlo baya kuzama ukuxoxa kangangoko kunokwenzeka. Ukongeza, ize nibuzise ukuba ngubani na sifo kwizigulo, kukho iindlela ukuphepha loo inkathazo apho.

Yintoni myasthenia gravis?

Myasthenia gravis sisifo samathambo ebangela ngcembe buthathaka kwezihlunu. Oku kwenzeka ngenxa lokungaphumeleli xa idluliselwa neuromuscular. Kwiimeko ezininzi, izihlunu uchaphazelekayo yamehlo, iintsini, ubuso, ubuncinane - ekwenzeni umsebenzi sokuphefumla.

Njengoko manani zibonisa, myasthenia gravis kudla kuchaphazela amabhinqa phakathi kweminyaka, nangona kwiminyaka yakutshanje yaso ibhalwe phakathi abaselula.

nokubekwa kwezifo

Phantse wonke sifo zihlelwa uhlobo. Mna ke kungekho ngaphandle, yaye myasthenia gravis. Uhlobo sifo kunokuxhomekeka izinto ezahlukeneyo, ngoko ke, siya sijonga ezivame.

Kuxhomekeka iqela beminyaka beqela myasthenia nomonde gravis ingaba:

  • bekhubazekile;
  • kubelekwa;
  • ulutsha;
  • abadala;
  • version kamva.

Kuxhomekeka imiqondiso kwezonyango sifo iintlobo ekuthiwa myasthenia gravis zilandelayo:

  • shape amehlo;
  • musculoskeletal;
  • pharyngeal-ubuso;
  • ngokubanzi.

Iimpawu ngalinye iintlobo zesi sifo kuxoxwa ngezantsi.

Ezibangela isifo

ingcambu unobangela izifo nangoku uhlala unexplored. Yinto eyaziwayo nje ukuba esi sifo kwenzeka ngenxa ukuvaleka receptors amajoni omzimba kwi izihlunu. Ngenxa yoko, abakwazi ukuba ukusabela kwisiphumo se imiyalezo uvaleke.

Isifo myasthenia gravis kunokuba iziphene okanye lufundiwe. Ifomu yokuqala anqabe kakhulu, noonobangela zayo kwiDNA.

myasthenia Acquired gravis ngazo ngokwayo phezu thymomegaly yangasemva (ingozi hyperplasia prostatic, thymus) okanye ngamathumba. Ngokuqhelekileyo, unobangela esi sifo kuba isifo samathambo, ezifana scleroderma okanye dermatomyositis.

Kukho iimeko ezininzi xa myasthenia gravis kujongwe kwimvelaphi zomhlaza. Ngokukodwa, kumayelana ithumba amalungu obuni (yesinye, maqanda), ubuncinane - isibindi, umphunga, njalo-njalo.

iimpawu

Yintoni imiqondiso kuya kukunceda ukuba wenze isifo, "gravis myasthenia"? Iimpawu inokuba nomahluko okanye idityaniswe ngokuxhomekeke ifomu kunye ibakala sifo.

myasthenia ocular gravis kuchaphazela:

  • setyhula umsipha iso;
  • izihlunu amehlo ;
  • imisipha, nenoxanduva nokuphakamisa ijwabu eliphezulu.

Ngenxa yoko, iimpawu olu hlobo sifo ngolu hlobo lulandelayo:

  • ubunzima ekujoliseni amehlo;
  • strabismus;
  • andiboni kakuhle;
  • nakwenzeka ixesha elide ukujonga izinto ezikude mhlawumbi esondele kakhulu;
  • netshiki of ijwabu eliphezulu (ptosis).

Ekugqibeleni iimpawu ingqalelo ngazo ngokwayo kuphela ngokuhlwa kunye ndingekho ngokupheleleyo kusasa.

uhlobo phambi myasthenia gravis sikhatshwe ziimpawu:

  • utshintsho ilizwi, nto leyo iba i "impumlo" kunye iimfama;
  • ingxaki (isigulane eziva ediniwe emva kwemizuzu embalwa incoko);
  • ubunzima kunye ekudleni (isigulana kunzima kakhulu ukuba ukuhlafuna ukutya okuqinileyo ngenxa yobuthathaka esihlunwini ahambelanayo).

Emva kokoyiswa pharynx kukho amathuba aphezulu lingenwe amanzi kwisiqwenga sokuphefumla. Oku kubangelwa yinto yokuba isigulane engakwazi ukuthatha ukutya okuqinileyo kwaye ano-, okwenzeka kaninzi. Ngenxa yoko, oko igcwele kunye nophuhliso yokulangazelela pneumonia.

uhlobo Musculoskeletal esi sifo ihamba adinwe ngexesha yinxalenye ethile yomzimba. Kwiimeko ezininzi, oku kusebenza imilenze. Kukho iimeko xa isigulane abakwazi ukuthatha indebe eqhelekileyo amanzi okanye bakhwela kwizinyuko.

Kuyingozi kakhulu luhlobo jikelele kwesi sifo. Kubonisa imposiso izihlunu nokuphefumla, nto leyo enokukhokelela ekubeni hypoxia etsolo nokufa.

Njengoko ubona, myasthenia gravis, iimpawu zazo kakhulu ezahlukeneyo, i izifo kunobuzaza kakhulu futhi ezisongela ubomi. Yiyo loo nto kubalulekile ukuba kuqatshelwe ukuvela le ngxaki kwaye athathe onke amanyathelo ayimfuneko.

Ngoko ke, ezi zinto zilandelayo eziya kuxutyushwa sikhokelo othi "Myasthenia Gravis", - Uxilongo kunye nonyango lwesifo.

isevisi ayikho

Myasthenia Gravis - oku kakhulu sisifo esinqabileyo. Ngoko ke, lo luvo akakwazi akusoloko bakhawuleza ukwenza ukuxilongwa echanekileyo.

Yintoni ekufuneka yenziwe ukuba ukuchonga zempilo ezifana myasthenia gravis? Uxilongo kungabandakanya:

  • uphando sesigulane ebusweni izikhalazo;
  • kuxilonga;
  • prozerinovoy sokwezela uvavanyo;
  • Uvavanyo ne edrophonium;
  • isifundo electromyographic;
  • izigqibo kwinqanaba antibodies receptors acetylcholine kwi serum;
  • ukuhlolwa amehlo;
  • Itomography ngekhompyutha kwesifuba;
  • MRI;
  • khangela umsebenzi lung.

Ngexesha isifundo, kubalulekile ukuphelisa zonke izifo kunokwenzeka, iimpawu ezibangela othile efanayo iimpawu myasthenia gravis. Umzekelo, kusenokuba syndrome bulbar, izifo ukudumba (meningitis, kobuchopho), ithumba uluhlu esikhondweni ebuchotsheni (hemangioblastoma, glioma), neuro-eqatha sifo (myopathy, Guillain syndrome, ALS, njalo-njalo), isifo cerebrovascular (instult kobuchopho ) njalo njalo.

unyango ngamachiza kwe myasthenia gravis

Kuxhomekeka iimpawu, kunye ibakala esi sifo kuyohluka kwaye uhlobo olufunwayo unyango.

Indlela yokuqala ufuna iziyobisi ukuphucula ukudluliselwa angxamele kwi ezidibanayo neuromuscular. Kaninzi zisetyenziselwa le njongo arhente amayeza afana "oksazil", "Neostigmine" "Pyridostigmine" njalo-njalo. bonke ibenodidi efanayo yesenzo nokunyusa uyondelelwano lwee- acetylcholine. La machiza kakhulu ngempumelelo ukubatshabalalisa sifo nisaqala wophuhliso lwawo, kwakunye nangexesha lokubhalwa uhlaselo iingxaki.

Into elandelayo ekufuneka uyenze - ilungelo ukunyenyisa eseleyo amanzi kunye electrolyte emzimbeni. Oku kuya kufuna ukutya okwaneleyo kuye iivithamini B kunye potassium ukuqinisekisa ukutya yesiqhelo.

Ukuqhubela phambili kwesi sifo kubandakanya ukwenziwa kwamanyathelo unyango ndlongondlongo ngakumbi. Bona akumi ulwamkelo iihomoni immunosuppressive. Nangona la machiza abalufumani zivunwe umzimba, ingenelo ukusebenzisa kwabo iziphumo lukhulu ibangela, ingakumbi xa kuziwa kwimpilo nje kuphela, kodwa ubomi.

Ziqapheleni!

Kukho ezinye iziyobisi azivumelekanga ngqo ukwenza uxilongo "myasthenia gravis". Ezi ziquka beta-blocker, iityuwa nemagnesium, abamelene calcium, nemithi, aminoglycosides, hormone, uxinezeleko, morphine, avela umkhwinini, antipsychotics, barbiturates, yaye uninzi hypnotics kunye nadlamkisayo.

Ukongeza asimele, silibale ukuba nasiphi na isiyobisi zamachiza zingasetyenziswa kuphela emva kokuba kuqeshwe kwagqirha, kuthathelwa ingqalelo zonke iimpawu ngabanye eziphilayo.

Unyango nge utyando

Unyango ngamachiza asisoloko kuwucima, kwaye ukuphelisa le ngxaki. Ngoko ke, oko kudla kuyimfuneko ukuba ungenelelo yotyando. Ngoko, ke, ungaquka ubambe enye okanye iinkqubo ezininzi:

  • yomatshini xa ukungakwazi ukuphefumla ezizenzekelayo;
  • igazi plasmapheresis ocwenga omzimba ezingaqhelekanga, apho inkqubo kufuneka wenziwe rhoqo rhoqo;
  • therapy emsebenzini kunye physiotherapy - ezi nkqubo zimbini azisusi esi sifo, kodwa unako ukunceda isigulane ukumelana ukuhla ngamandla kwezihlunu.

Ukongeza, kusenokuba yimfuneko ukususa esinobubovu thymus ngokusebenzisa uqhaqho.

Isiqu therapy cell

Olu hlobo ukubatshabalalisa ingxaki akukabi nawo kakhulu, kodwa kubalulekile ukukhumbula kwaye ngaye.

Treatment kunye iiseli stem evela izihlunu adipose, lubonise ukusebenza ngokwaneleyo phezulu ekulweni nezifo. Eziphuhlisa ngayo ukwandiswa iphezulu ixesha kuxolelwe. iiseli stem Healthy ukunceda iinkqubo lokulungiswa zokuphefumla ligwinya. Ukongeza, ukuba igalelo ekupheliseni ptosis kweli xesha lifutshane kangangoko kunokwenzeka.

Ikhosi ye unyango kunye rhoqo ulawulo kweeseli isiqu umzimba ukwabela kuphela specialist abanamava!

Liqikelele elizayo

Nkqu ngenkulungwane yokugqibela, lokufunyaniswa "Myasthenia" kwakuthetha ukuba uza kufa. Kodwa ke, ekuhambeni kwexesha, kunye namayeza na ukuma. Okwangoku, sisungule ezahlukeneyo iimveliso ezikhethekileyo ezinceda ukugcina ubomi nokwandisa ithuba kuxolelwe.

Ngelo xesha ke kufuneka ungalibali ukuba gravis myasthenia sisifo esingapheliyo. Oku kuthetha ukuba izigulane ziya kuba lonke ixesha kuba phezu unyango (okanye irhafu rhoqo) ukugcina impilo. Asinto kunzima ukuthelekelela ukuba umgangatho wobomi kule kunokwenzeka ubunzima kakhulu.

Ngoko kuyimfuneko ukuba ukuyibethelela eyokuba kuphela uxilongo ngexesha esi sifo enokuthintela progression yayo ngendlela ngexesha siphephe iingxaki.

uthintelo zingabuyi

Sasidla ngokuthetha ngalo ngezifo njengoko myasthenia gravis. Yintoni na, oko sikhatshwa iimpawu zokugula kunye nokuba kukho unyango olusebenzayo zesi sifo, kuyaxoxwa. Ekugqibeleni Ndingathanda ukuba zihlale phezu iindlela zothintelo ndiphinde ndazisebenzisa, njengoko kwizigulana, isihloko efanelekileyo kakhulu.

Okokuqala, ingxelo ebalulekileyo kwi-akhawunti ukuya luvo. Kulo mzekelo, nakweyiphi imeko zilubona ubuchule ezicwangcisiweyo, kodwa xa kuthe iimpawu kufuneka uqhagamshelane nogqirha ukulwa, hayi elinde kutyelelo olulandelayo.

Okwesibini, kufuneka ukuba kwakhona kwaye, ukuba kuyimfuneko, lungisa ubomi bakho obuqhelekileyo. Izigulane myasthenia kwazo naziphi na iimeko ukuba kukho ukudinwa emzimbeni, ngoko kuyacetyiswa ukuba ukhethe umsebenzi, enika umsebenzi engqondweni. Ukuba kunokwenzeka, kufuneka anciphise ixesha uhambo, ingakumbi ngokubhekiselele kwizithuthi zikawonke.

Asimele silibale ukuba nasiphi na isifo, nkqu SARS, ebangela uxinezeleko umzimba kunye nokuphazamiseka kwamajoni omzimba. Kubalulekile ke ngoko ukuba esweni ngokusondeleyo nemeko yempilo yabo, ukuthintela emzimbeni kwaye ukuba iindawo zoqhaphelo olukhulu zabantu bexesha ukuxhaphaka jikelele kwezifo ezosulelayo.

Phambi myasthenia gravis ofumana naluphi iyeza kufuneka kuvunyelwane nogqirha wakho, ngenxa yokuba kukho Izimo ezikhethekileyo ezininzi (abathile bakhumbula phezulu kubo).

Musa self-medicate futhi ube nempilo!

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