ZempiloDiseases and nemibandela

Isifo Kick - ntoni na?

Kukho izazinzulu banamhlanje siyakholelwa ukuba zonke namabali nezithunzela kuba kwezesayensi. Banokwenza kuba phantsi kwempembelelo sifo enqabileyo efana nesifo Gunther okanye "porphyria cutaneous." Esi sifo olonakalisayo igazi, besusa uchuku kwi yokuzala kule gem. Kukholelwa ukuba isifo Gunther kaThixo eqhelekileyo kakhulu kwiilali encinane yayo. Apho ke kuvela zonxibelelwano ezinxulumene ngokusondeleyo.

Iingcali zithi ukuba esi sifo, abasoze unawo nawaphi na amabali kunye neentsomi of nezithunzela, Dracula kunye namanye amaqhawe kunye aso. Phantse bonke isigulane nazimpawu ngubani iqalile ngamandla sisifo Gunther kaThixo - a iimovie vampire eqhelekileyo.

Fumana unobangela ngxaki, kwaye uchaze sifo sikwazi kuphela kwinkulungwane yama-20. Ngaphambi koku kuthwalelwa ukulwa nabo nezithunzela: ukususela 1520 ukuya 1630 eFransi kuphela babulawe ngaphezulu kwama-30 amawaka abantu, abo ingqalelo nezithunzela. I ngakumbi lizwe kweza ubuKristu, kokukhona ngakumbi ufekethe ngokubaphatha kakubi abantu owoyisa porphyria cutaneous emva kwexesha.

Kule fomu ezinqabileyo sifo yemfuza ngenxa umntu omnye kuphela amawaka 200 nganye. Kulo mzekelo, xa kukho ingxaki eso ukubandezeleka omnye wabazali, ngoko ke sithethe i-25% kakuhle ukuba isifo Gunther likaThixo kunye nomntwana.

Kukholelwa ukuba le sifo - isiphumo kwezihlobo. Medicine ichaza malunga 80 amatyala porphyria etsolo xa kwakungenakwenzeka ukuba ukunyanga. isifo Kick bukaThixo luphawulwa yinto yokuba umzimba ayisebenzi iinkalo eziphambili igazi - ezibomvu iiseli zegazi. Kwaye oku kubonakala ukunqongophala zentsimbi kunye ioksijini egazini.

In ancedisana igazi Kukuyihlambela sombala ukutya nangenxa kwelanga kuqala iba mpilo. Ukongeza, le nkqubo lwenzeka ubunzima imicu ekhokelela ukugoba leminwe kwezinye iimeko.

isifo Kick bukaThixo luphawulwa kukuba GEMS (non-protein inxalenye mpilo) uguqulwe into ityhefu, nto leyo ezinokudla inyama ongama. Ngenxa yoku, isikhumba uba omdaka ngebala, mlomo kunye ikhefu emva lwaphumelela kwelanga. Ngenxa yesi sizathu, ngokuhamba kwexesha isikhumba ezigqunyiweyo ngokupheleleyo izilonda yako. Ukongeza, komtshiso oko kungonakalisa iindlebe kunye impumlo, deforming ngokuqatha kubo.

Masithi umntu iinzwane zijonge nobuso egcwele izilonda ... Nyhani kuyoyikisa? izigulane ezinjalo contraindicated nje kwelanga, kuba oko kubenza ukubandezeleka okukhulu. Isikhumba, ibekwe ngeenxa iintsini kunye nemilebe liqiniswe yaye owomileyo. Ngenxa yale phantsi iintsini uyihlubile siphume, ukudala vampire wagqabhuka eyoyikekayo.

Olunye uphawu lwesi sifo: amazinyo elinye porphyrin, ngenxa yesi sizathu, bazithengele umbala obomvu nokuba zifuna ukuba ngqombela-mdaka. Ogulayo kakhulu eluswini libunile inshorensi. Emini baziva silale enamandla kunye nokungabikho lwamandla, amandla ibuyiswa kuphela ebusuku. Kubalulekile ukuphawula ukuba yonke isethi iimpawu uphawu kuphela sifo xesha lamva. Kukho olunye uhlobo, ngaphantsi kakhulu eyoyikekayo porphyria.

Kude kube kwisiqingatha sesibini senkulungwane yama-20, isifo Gunther kwakugqalwa phantse esinganyangekiyo. Kukho ubungqina bokuba kwi kumaXesha Aphakathi, ukuququzelela imeko yomguli wanikwa igazi entsha makasizalise yokunqongophala iiseli zegazi. Ngokwendalo, oku akuzange ukunika naziphi na iziphumo, ngenxa yokuba imeko eziphuculweyo igazi, ukusela nje isabelo sakhe, akunakwenzeka.

Izigulane ne porphyria makangayidli ikonofile, ngokuba esiti, ephuma le imifuno, ukunyuka ezibangelwa umonakalo izifo. porphyria sifo kungabangela okwenziwe, usebenzisa i tyhefu ethile kunye neekhemikhali.

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