ZempiloIzifo neemeko

Ichthyosis yeHarququin kunye nezinye iintlobo zesifo esibi

Ngaphantsi kwe-ichthyosis kukuphulwa kweekatatini zesikhumba sesikhumba. Kuboniswa ngamaziko athile, onke akhangeleka kakhulu njengezikali zeentlanzi. Iphuma njenge-dermatosis kwaye inokudluliselwa ngelifa.

Isifo esibonakalayo singadlula ixesha okanye sibe sesibindi (Harlequin ichthyosis). Izizathu ezichanekileyo zeziphumo zalo azikabikwa. Ngokuchanekileyo, kunokuthiwa ikhula ngenxa yokuguquka kwemfuza. Inani elininzi ngokwe-amino acids egazini likhokelela ekubeni iprotein ye-metabolism iphazamiseka, kwaye ngenxa yokungaphezu kwe-cholesterol, utshintshiselwano lwamafutha luphazamiseka. Ezi zibonakaliso zibonakaliso zokungasebenzi kwemvelo ezingakhokelela kwi-ichthyosis.
Ukufudumala kwezigulane kuphazamiseka. Ngenxa yokusebenza ngokweqile kwee-enzyme, iinkqubo zokuphefumula kwesikhumba zikhawuleza, zikhona iingxaki kwi-thyroid gland, i-adrenals, i-glands. Phantse njalo unako ukugcina ubuninzi bekeratin, obunokwehlukileyo kwisakhiwo.
Nge-ichthyosis, iiseli ezifile ziyanqatshwa kakhulu. Ngenxa yesi sizathu, isikhumba siqala ukuvela kwisikali se-horny. Ngexesha, i-amino acid complexes iqala ukuqokelela phakathi kwabo. Ulusu lukhuni kule nto. Imfundo iqhotyoshelana, ukususa kwabo buhlungu.

Ichthyosis yeHarlequin

Le fomu yesifo yona inzima kakhulu. Inyaniso kukuba i-Harlequin ichthyosis ikhula kwi-fetus, esesibelekweni sikamama. Esi sifo sizuze kwi-autosomal type excessive. Imbonakalo yayo yokuqala ingabonwa emva kweveki yeshumi elinesithandathu yokuphuhliswa kwe-intrauterine.
Ichthyosis yeHarququin ibangela ukuba ulusu lolutsha luba njengegobolondo. Le "ngqungquthela" iqulethe izikhuselo ezimnyama. Ubukhulu babo bunokufikelela kwisentimitha enye. Bona ngokwabo babhekiswe, bathebile, banzi.
Phakathi kwezikhalazo uyakubona ukusila. Ichthyosis iHarququin ichukumisa yonke indawo yomzimba kunye nobuso. I-predict in this case ayikho embi kakhulu. Abantwana bafa kusasa. Oku kungenxa yokuba isifo esibi sisichaphazela zonke izitho. Ngokuqinisekileyo, ukuvela kule nto akunakwenzeka. Le ichthyosis nayo ibangelwa ukuguquka kwemfuyo. Kubantwana, zonke iinkqubo zomzimba ziyaphulwa, i-cholesterol iphakama. Ukungakhuselekanga kwalabo abazelwe kwesi sifo akunjalo, iifostile zithukuthela zibi kakhulu.

Vulgar ichthyosis

Le ntlobo ixhaphake kakhulu kunezinye. Ilifa. Impawu zokuqala zalo zingabonwa kwinyanga yesithathu yobomi bomntwana. Kwezinye iimeko, iimpawu ziqala ukubonakala kamva.
Ngaloo ndawo, ubuso besikhumba bome, buba bubi kwaye buhlanganiswa nezikali. Umntu, njengomthetho, akamangalisi. Izigulane zinengxaki ezintso, isifo senhliziyo, isibindi.

I-ichthyosis edibeneyo ye-X

Kubonakala kuphela kubafana. Iimpawu zokuqala zingabonwa kwiveki yesibini yobomi. Kulo hlobo, izikali ezimnyama ezimnyama esikhumbeni ziyimpawu. Ulusu lubukeka njengenyoka okanye ingwenya. Esi sifo sinokuhamba kunye nokuhluthwa, kunokukhokelela ekulibazisekeni ekuphuculweni kwengqondo.

Ichthyosis: unyango

Yonke into incike kwixinzelelo yesifo ngokwayo. Ukunyangwa kwe-ichthyosis kunokwenziwa kwisitishi esisigxina okanye sokugula. Izigulane zinqunywe i-vitamin ende. Iziyobisi zePotropic nazo ziyalelwe - oku kunceda ukuphepha ukuqiniswa kwezikali. Amanyathelo athatyathwa kwakhona ukubuyisela umzimba.

Maxa wambi amayeza e-hormone asetyenziswa. Kulo unyango lwengingqi lungathunyelwa kunyango lwama-flake kunye ne-potassium permanganate, i-cream cream kunye njalo.

Esi sifo siphuthuma ngokukhawuleza, oko kuthetha ukuba ukuhlaziya kuya kubangela ukuba iinjongo zangaphakathi nazo kufuneka ziphathwe.

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