Zempilo, Diseases and nemibandela
ALS (disease): Iimpawu kunye nendlela isifo
I-luvo abantu abasengozini kakhulu. Kungenxa yoko le nto kukho izifo ezininzi ezahlukeneyo kuchaphazela le yinxalenye ethile yomzimba. Kweli nqaku ndifuna ukuthetha into ALS (disease). Iimpawu, unobangela izifo, ngokunjalo iindlela isifo kwaye afumane unyango kunokwenzeka.
Yintoni na?
Ekuqaleni, kufuneka baqonde iingqiqo esisiseko. Kwakhona kubalulekile kakhulu ukuqonda ukuba yintoni i-BAS (disease), iimpawu zesi sifo kuya kuxoxwa kancinane emva koko. Ingcaciso izifinyezo: lateral atrophic sclerosis. Xa esi sifo sichaphazela indlela luvo yomntu, oko kukuthi ubunzima luvo motor. Bona akhiwe neuron kwaye iimpondo Icipande umnqonqo. Kubalulekile kwakhona ukuba sikhankanye ukuba isifo ezingapheliyo, ngelishwa, ngalo mzuzu alinyangeki.
iintlobo
Kukho iintlobo ezintathu sifo ezifana ALS:
- zakudala khona. It is hhayi ilifa. Loo nto yabangela ukuba malunga nama-95% yazo zonke iimeko izifo.
- Sofuzo (okanye usapho). Njengoko libonakele, kuba ilifa. Nangona kunjalo, olu hlobo sifo sizibonakalisa ngembonakaliso kamva iimpawu.
- Guam-uhlobo okanye nokumila Mariana. osemqoka efana sibonakalaliswe phambi kwesihlalo ezimbini ngasentla. uphuhliso Slow esi sifo.
I Iimpawu zokuqala
Iyafuna esithi ukuba iimpawu zokuqala zesi sifo kunokunyangwa kwaye nasiphi na izifo. Yiloo nto kanye ingxaki inkohliso; ukuxilonga kwangoko kuba nzima. Ngoko ke, iimpawu yokuqala ALS zimi ngolu hlobo lulandelayo:
- Muscle ubuthathaka. Ngokomthetho kuziwa kwamaqatha nasezinyaweni.
- Yoma izandla, ubuthathaka izihlunu. Kwakhona kuthi dysmotility.
- Izigulane kwi zigaba yokuqala sifo Alenga kancinane stop.
- Lubonakala periodic aqaqambayo. Ngaba ukudideka emagxeni akhe, izandla, ulwimi.
- Omzimba buthathaka. Isigulana nzima unako ukuhamba imigama emide.
- Kwakhona iimpawu imbonakalo dysarthria, ngamanye nentetho engekho mgaqweni.
- lokuqala igwinya nzima kuthi.
Ukuba ogulayo ALS (a isifo), iimpawu kuphuhliso sifo iza kuphuhlisa, ikhule. Okulandelayo, isigulane maxa wambi baba ukulwa kumnandi okanye unxunguphele. Yoma zingenzeka ulwimi kunye disequilibrium. Konke oku kungenxa yokuba umntu ukubandezeleka umsebenzi eziphezulu engqondweni. Kwezinye iimeko, phambi kokuba kukho iimpawu ezinkulu uphazamise umsebenzi kwengqondo. ie sengqondo esixhalabisayo ivela (oku kwenzeka ngamaxesha athile, nama-1-2% amatyala).
phambili kwesifo
Yiyiphi enye into ebalulekileyo kukuba ukwazi abantu abanomdla ALS (izifo)? Iimpawu ezifumaneka kwi isigulane njengoko sifo enokuthethwa yintoni kanye uhlobo wakhe izifo:
- omzimba ALS. Umlenze lokuqala kwenzeka soyiswa. Eminye liphakama umsebenzi ukungathobeli lomzimba.
- ALS Bulbar. Kulo mzekelo, iimpawu eziphambili zezi umsebenzi intetho ukungathobeli, kwakunye nengxaki ligwinya. Iyafuna esithi olu hlobo sifo azixhaphakanga kunesiqalo.
ukwanda nezimpawu
Yintoni ekufuneka uyazi ukuba isigulana umntu nesifo ALS? Iimpawu ziza kwanda, yalityatya ngokwamathambo functionality iya kuncitshiswa.
- Ngokuthe ngcembe apho yezifo Babinski, xa nale luvo motor eliphezulu.
- kwezihlunu, ikhaliphe ziza kuphuculwa ukuze ziphuculwe.
- Ngokuthe ngcembe uya kuba luvo motor nqa ngokuhla. Kulo mzekelo, isigulane uzakuva kuxhuzula kwezi ngokuzenzekelayo le imilenze.
- Kule pretty ngokufuthi abantu abagulayo kukudakumba, kukho ukudangala. Zonke kuba Umntu uyaphelelwa ubuchule ukuphila ngaphandle kwalo naluphi na uncedo, oko baphulukana nako ukuqhubela.
- Iimpawu ALS zinxulumene isixokelelwano sokuphefumla: isigulane uqala uphefumla iziphazamiso.
- Kwakhona, akunakwenzeka ukuba self-catering. Isigulane isoloko sifakwe ityhubhu apho indoda ifumana zonke izinto eziyimfuneko ukuze ubukho ukutya.
Iyafuna esithi ALS ezintle kungenzeka msinyane. Iimpawu eselula akayi kuba kwahluka iimpawu yesigulane, imiqondiso yabo yokuqala ukuvela kakhulu kamva. Konke kuxhomekeke emzimbeni, kwakunye kuhlobo sifo. Ngophuhliso sifo ngokuthe ikhubaze Umntu uyaphelelwa amandla zokuphila ezizimeleyo. Ekuhambeni kwexesha, wakhanyela ngokupheleleyo lomzimba.
Isigaba sokugcina
Kumanqanaba okugqibela esi sifo isigulana rhoqo umsebenzi kakuhle nokuphefumla, ukungaphumeleli izihlunu zemiphunga kunokwenzeka. Kwiimeko ezinjalo, izigulane kufuneka umoya. Ekuhambeni kwexesha, nga umsebenzi kutsalwe umzimba, nto leyo ngokufuthi ekhokelela ukuba ajoyine iqela usuleleko lesibini, nto leyo ubulala umguli.
ekuxilongweni
Ekubeni ingqalelo nesifo ALS, iimpawu, uxilongo - yiloo nto ndifuna ukukuxelela nayo. Iyafuna esithi ukuba esi sifo ifunyanwa kaninzi inkqubo ukuphelisa ezinye iingxaki kunye nomzimba. Xa isigulane ezilandelayo iindlela zokuxilonga ukuze yabelwe:
- test Blood.
- Muscle biopsy.
- X-ray.
- Uvavanyo ukuqinisekisa umsebenzi kwezihlunu.
- CT, MRI.
kuphakanyiswa
Iyafuna besithi sifo uneempawu esinokwenzeka kunye nezinye izifo. Kuyimfuneko ke ngoko ukuba umahluko ALS nezi ngxaki zilandelayo:
- myelopathy wesibeleko.
- Ukunxila ngu mercury, ilothe, manganese.
- bar Syndrome nakoodyakalashe.
- Malabsorption syndrome.
- Endocrinopathy et al.
unyango
Bit ingqalelo nesifo ALS, iimpawu, unyango - oku kufuneka ukuba anikele ingqalelo ekhethekileyo. Njengoko sele kukhankanyiwe ngentla apha, ongayi kuba nako ukuphiliswa ngokupheleleyo. Nangona kunjalo, kukho iziyobisi ukuba wehlise ekuhambeni sifo. Kulo mzekelo, izigulane ngokufuthi kuthatha amayeza afana "Riluzole", "Rilutek" (yonke imihla kabini ngosuku). Oku uyakwazi ukuthintela imvula of glutamine kancinane, into esichaphazela luvo motor. Noko ke, kwakhona iluncedo iindlela zonyango, enjongo yayo engundoqo - ekulweni iimpawu eziphambili:
- Ukuba isigulana odakumbileyo, yena, lakhula, okudambisa kunokumiselwa.
- Xa izihlunu spasm kubalulekile ukuthatha relaxants kwezihlunu.
- Ukuba kuyimfuneko, zomzimba linokukwenziwa, xa kade inqanaba lesi sifo - opiates.
- Ukuba isigulane iye yaphazamiseka ubuthongo, kufuneka iziyobisi benzodiazepine.
- Ukuba kukho ingxaki igciwane kufuneka antibiotics ukutya (nge bass badla izifo bronchopulmonary).
Aids:
- Speech therapy.
- Slyunootosos okanye ukufumana iziyobisi ezifana "Amitriptyline".
- Tube ukutya, ukutya.
- Ukusetyenziswa kwezixhobo ezahlukeneyo ezinokunika intshukumo nomonde: iibhedi, izitulo, izinti ehamba, iikhola ezizodwa.
- Ngamana kufuneka umoya ngomatshini.
amayeza emveli, lokugqojozwa esi sifo zizinto ezingento nje. Kufuneka kwakhona wathi kuphela isigulane kodwa intsapho yakhe badinga uncedo nomntu owayendifundisa.
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