Kubazali bakhe kubantwana - bekhubazekile pathology igazi

Kubazali bakhe kubantwana - ilifa ukopha diathesis. Uphuhliso kubazali bakhe ibangelwa ukuswela naso kwemiba igazi ababandakanyekayo ekubunjweni plasma thromboplastin, into efunekayo ukuze igazi nciphisa ngokukhawuleza trauma.

Isifo kwenzeka ubukhulu becala ngabantu. Isasazeka ukusuka abazukulwana abagulayo ngokwezonyango iintombi esempilweni. Kukho iintlobo ezintathu kwesi sifo.

1. kubazali bakhe A - lolona hlobo luqhelekileyo kwesi sifo. Ngenxa ukungaphumeleli antihemophilic igazi globulin yesigulane.

2. kubazali bakhe B ibangwa ukuswela kwi candelo thromboplastin plasma yegazi.

3. kubazali bakhe kuba kubangelwa kukungabikho plasma yegazi thromboplastin kuneyokuqala.

Ngenxa insufficiency egazini enye yezi meko iphazamisekile coagulation yakhe. Eli igazi eqokelelwe kwityhubhu uvavanyo, akuthethi ihlwili ixesha elide kakhulu, yaye izinto ukusekwa ngokuthe ngcembe ezantsi.

Esi sifo luphawulwa uhlobo gematomny ukopha. Eyona isikhalazo lwezigulane - umkhuba ezophayo, esizibonakalisa kunye minyaka yokuqala yobomi. Xa kwimbali kubazali bakhe ebantwaneni ubonisa intambo ukopha, hematoma ekuzalweni, Imihla iyoluka ukopha iinkathazo ezingenakunqandwa zamazinyo, amanxeba isikhumba. Kamva ukuvela ukudumba nokuthantamisa namalungu kunye iingozi ezincinane. Abantu abadala bagcina ebuhlungu enkulu nokopha kwi izihlunu ongama, hematoma kwezihlunu. amanxeba ukopha Ngaphantsi elintlangothi batyumke. Oku kungenxa yokuba kukunqongophala plasma thromboplastin ngokungaphelelanga zincitshiswe ukhupho ebalulekileyo kwithishyu.

ukopha bokugcinwa inwebu yangaphakathi emlonyeni, impumlo, iphecana zesisu, zezintso, bronchus. Kunokwenzeka Ukopha ebuchotsheni okanye meninges. Ezisongela ubomi retroperitoneal hematoma yesigulane, ukopha engcanjini ulwimi, intamo, umqala. ukopha ezimandundu kunokubangela nayiphi izakhi zonyango, umz, ukususwa izinyo, inaliti ezahlukeneyo, kwaye ingakumbi uqhaqho. A feature of ukopha syndrome xa kukho umonakalo iinqanawa ezincinane kamva ivela ukopha. Inokuba ngaphakathi kweeyure ezimbalwa emva kokwenzakala.

Iimpawu ekuqhelekileyo ukuba kwenzeka abantwana kubazali bakhe ukopha ezingenantloko, ebizwa hemarthroses. Amaninzi ukuphuhlisa hemarthrosises amadolo kunye namalungu ingqiniba. La ibuhlungu kakhulu, sikhatshwe ukunyuka kwamaqondo obushushu. hemarthrosises ephindiwyo kukhokelela kuphuhliso contractures.

Kubazali bakhe - isifo igazi kakhulu. kubazali bakhe ingakumbi kakhulu ebantwaneni nakulutsha. Kwixesha elidlulileyo, izigulane ezininzi babulawa ukopha okanye legazi kwi izibilini de kwiminyaka engamashumi amabini. Iingxaki sifo zibandakanya igazi kakhulu kunye izitshanguba namalungu - hemarthrosis kunye contractures asakhulayo hemarthrosis.

Ukuba unesifo kubazali bakhe, unyango kufuneka wenziwe kunye kwiinyanga zokuqala wobomi isigulane. Indlela engundoqo ukunyanga ukopha an unyango replacement engxamisekileyo. Kuba unyango kubazali bakhe usebenzisa iimveliso igazi, apho imiba coagulation igazi zinto ziqwetyelwe, zigcinelwe ngaphezu igazi elitsha. Le plasma antihemophilic, cryoprecipitate okanye igazi ekunqandeni factor mxube. Kwiingozi ezimasikizi, maxa wambi kusetyenziswa ngqo igazi exhasanayo. Xa kubazali bakhe B no-C ephathwa plasma lweenkobe kunye owomileyo, kwakunye nokulungiselela ezintsonkothileyo, equlethe izinto ezininzi ekunqandeni igazi. Ukusuka kwezinye izinto haemostatic kusetyenziswa aminocaproic acid kunye lwefibrinogen. unyango kubazali bakhe ithintela uphuhliso iingxaki izifo, iphucula kakhulu umgangatho kunye nobude bobomi malunga nesigulane eso.